2026 ICD-10-CM Diagnosis Code Q63.1Lobulated, fused and horseshoe kidney

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q63

ICD-10-CM Q63.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q63.1 is a billable ICD-10-CM diagnosis code for lobulated, fused and horseshoe kidney. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. Coders also document this condition as cake kidney. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q63.1
Billable Status
Yes — Valid for Submission
Code Describes
Lobulated, fused and horseshoe kidney
Short Description
Lobulated, fused and horseshoe kidney
Same as the full description in the CMS dataset.
Parent Code
Q63
Other congenital malformations of kidney

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ63Other congenital malformations of kidney
This CodeQ63.1Lobulated, fused and horseshoe kidney

Present on Admission (POA)Billing

Q63.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cake kidney
  • Congenital fusion of kidneys
  • Congenital lobulation of kidney
  • Crossed ectopia of kidney with fusion anomaly
  • Ectopic kidney
  • Horseshoe kidney

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cake kidney
    • Clump, kidney
    • Fusion, fused(congenital)
      • kidneys (incomplete)
    • Horseshoe kidney(congenital)
    • Lobulation(congenital)
      • kidney,
    • Malformation(congenital)
      • kidney
        • horseshoe
    • Ren
      • arcuatus
    • Ren
      • unguliformis
    • Shield kidney
    • Sigmoid
      • kidney

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Horseshoe Kidney

    a congenital abnormality in which the two kidneys fuse together during fetal development to create a horseshoe-shaped structure.

Patient EducationClinical

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q63.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.3 Kidney anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q63.1Overview

Is Q63.1 (Other congenital malformations of kidney) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lobulated, fused and horseshoe kidney on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q63.1 group to?

When lobulated, fused and horseshoe kidney is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q63.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for lobulated, fused and horseshoe kidney on inpatient claims.

What is the ICD-9 equivalent of Q63.1?

Under the General Equivalence Mappings, lobulated, fused and horseshoe kidney converts to ICD-9-CM 753.3 (kidney anomaly NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.