2027 ICD-10-CM Diagnosis Code Q61.5Medullary cystic kidney
ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q61.5 is a billable ICD-10-CM diagnosis code for medullary cystic kidney. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 4 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q61.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the urinary system (Q60-Q64).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Adolescent nephronophthisis
- Adult familial nephronophthisis with spastic quadriparesia syndrome
- Autosomal dominant tubulointerstitial kidney disease
- Bilateral medullary sponge kidney
- Boichis syndrome
- Congenital hepatic fibrosis
- Fibrocystic kidney disease
- Infantile nephronophthisis
- Juvenile nephronophthisis
- Medullary cystic disease of the kidney
- Medullary cystic disease, adult type
- Medullary sponge kidney
- Medullary sponge kidney with nephrocalcinosis
- Medullary sponge kidney without nephrocalcinosis
- MUC1-related autosomal dominant tubulointerstitial kidney disease
- Nephronophthisis
- Nephronophthisis - medullary cystic disease
- Nephronophthisis type 4
- Nephronophthisis type 5
- Nephronophthisis type 6
- Paresis of left lower limb
- Paresis of right lower limb
- RHYNS syndrome
- Spastic tetraparesis
- Tetraparesis
- UMOD-related autosomal dominant tubulointerstitial kidney disease
- Weakness of bilateral lower limb
- Weakness of left lower limb
- Weakness of left upper limb
- Weakness of right lower limb
- Weakness of right upper limb
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q61.5: its own notes plus those printed at Q61 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Nephronophthisis
- Sponge kidney NOS
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q61.5, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Cystic See Also: condition;
medullary Q61.5
medullary, kidney Q61.5
Medullary cystic kidney Q61.5
Nephronophthisis Q61.5
kidney (medullary) Q61.5
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Kidney Diseases, Cystic
a heterogeneous group of hereditary and acquired disorders in which the kidney contains one or more cysts unilaterally or bilaterally (kidney, cystic).
Patient EducationClinical
Kidney Cysts
A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q61.5 to ICD-9-CMHistory
Code HistoryHistory
Questions About Q61.5Overview
What is the ICD-10 code for medullary cystic kidney?
The ICD-10-CM code for medullary cystic kidney is Q61.5 (sometimes written as Q615). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q61.5 (Cystic kidney disease) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report medullary cystic kidney on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q61.5 group to?
When medullary cystic kidney is the principal diagnosis on an inpatient stay, it groups to MS-DRG 699, 698, 700, with relative weights from 0.6740 to 1.6400 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q61.5 a CC or MCC?
CMS lists Q61.5 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 4 closely related codes in its exclusion list.
Is Q61.5 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for medullary cystic kidney on inpatient claims. The code appears in the Congenital malformations of the urinary system (Q60-Q64) range of the CMS exempt list.
