2027 ICD-10-CM Diagnosis Code Q55.9Congenital malformation of male genital organ, unspecified
ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q55
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q55.9 is a billable ICD-10-CM diagnosis code for congenital malformation of male genital organ, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 729 through 730. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q55.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of genital organs (Q50-Q56).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- 11p partial monosomy syndrome
- 46,XY disorder of sex development
- 46,XY disorder of sex development due to environmental chemical exposure
- 46,XY disorder of sex development due to isolated 17,20-lyase deficiency
- Absent radius, anogenital anomalies syndrome
- Acrocardiofacial syndrome
- Agenesis of corpus callosum and abnormal genitalia syndrome
- Anal atresia
- Aphalangy, hemivertebra, urogenital, intestinal dysgenesis syndrome
- Aplasia of bone of radius and/or ulna
- Aplasia of radius
- Arachnodactyly
- Autosomal recessive facio-digito-genital syndrome
- B-cell immunodeficiency, limb anomaly, urogenital malformation syndrome
- Blepharophimosis, intellectual disability syndrome/genitopatellar overlap syndrome
- Cardiac urogenital syndrome
- Congenital absence of radius
- Congenital anomaly of male genital system
- Congenital anomaly of male urogenital tract
- Congenital cleft hand
- Congenital hypoplasia of adrenal gland
- Congenital malformation of genital organs
- Congenital obstructive azoospermia
- Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome
- Deletion of part of chromosome 11
- Disorder of sex development with intellectual disability syndrome
- Dysmorphism, short stature, deafness, disorder of sex development syndrome
- Frontonasal dysplasia sequence
- Frontonasal dysplasia with alopecia and genital anomaly syndrome
- Genitopatellar syndrome
- Genitourinary congenital anomalies
- Hand-foot-genital syndrome
- Harrod syndrome
- Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome
- Lethal hemolytic anemia and genital anomaly syndrome
- McKusick Kaufman syndrome
- MIRAGE syndrome
- Myotubular myopathy
- PELVIS syndrome
- RAB18 deficiency
- Short stature co-occurrent and due to endocrine disorder
- Spondylocostal dysostosis with anal atresia and genitourinary malformation syndrome
- STAR syndrome
- Telecanthus
- Urban Rogers Meyer syndrome
- WAGR syndrome
- X-linked lissencephaly with abnormal genitalia syndrome
- X-linked myotubular myopathy, abnormal genitalia syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q55.9: its own notes plus those printed at Q55, block Q50-Q56, and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Congenital anomaly of male genital organ
- Congenital deformity of male genital organ
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q55.9 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q55.9Overview
What is the ICD-10 code for congenital malformation of male genital organ, unspecified?
The ICD-10-CM code for congenital malformation of male genital organ, unspecified is Q55.9 (sometimes written as Q559). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q55.9 (Other congenital malformations of male genital organs) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of male genital organ, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q55.9 group to?
When congenital malformation of male genital organ, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 729, 730, with relative weights from 0.6595 to 1.0553 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q55.9 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of male genital organ, unspecified on inpatient claims. The code appears in the Congenital malformations of genital organs (Q50-Q56) range of the CMS exempt list.
Can Q55.9 be reported with P83.5?
Not as a rule. The Excludes1 note at Q55, which applies to Q55.9, lists "congenital hydrocele (P83.5)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
