Other congenital malformations of male genital organs (Q55) ICD-10-CM
The Q55 code range covers other congenital malformations of male genital organs with 21 ICD-10-CM diagnosis codes. 18 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q55 Range 21 codes · 18 billable
- Q55 Other congenital malformations of male genital organsNon-billable
- Q55.0 Absence and aplasia of testis
- Q55.1 Hypoplasia of testis and scrotum
- Q55.2 Other and unspecified congenital malformations of testis and scrotumNon-billable
- Q55.20 Unspecified congenital malformations of testis and scrotum
- Q55.21 Polyorchism
- Q55.22 Retractile testis
- Q55.23 Scrotal transposition
- Q55.29 Other congenital malformations of testis and scrotum
- Q55.3 Atresia of vas deferens
- Q55.4 Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
- Q55.5 Congenital absence and aplasia of penis
- Q55.6 Other congenital malformations of penisNon-billable
- Q55.61 Curvature of penis (lateral)
- Q55.62 Hypoplasia of penis
- Q55.63 Congenital torsion of penis
- Q55.64 Hidden penis
- Q55.69 Other congenital malformation of penis
- Q55.7 Congenital vasocutaneous fistula
- Q55.8 Other specified congenital malformations of male genital organs
- Q55.9 Congenital malformation of male genital organ, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q55 range.
Arachnodactyly
An abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. Arachnodactyly can include feet and toes. Arachnodactyly has been associated with several gene mutations and syndromes.
Priapism
A prolonged painful erection that may lasts hours and is not associated with sexual activity. It is seen in patients with SICKLE CELL ANEMIA, advanced malignancy, spinal trauma; and certain drug treatments.
WAGR Syndrome
A contiguous gene syndrome associated with hemizygous deletions of chromosome region 11p13. The condition is marked by the combination of WILMS TUMOR; ANIRIDIA; GENITOURINARY ABNORMALITIES; and INTELLECTUAL DISABILITY.
About the Q55 Code Range
The ICD-10 code Q55 category covers various rare congenital malformations affecting male genital organs, including the testis, scrotum, penis, vas deferens, and related structures. These codes help specify conditions such as absent testes, hypoplasia of genital organs, and unusual structural anomalies present at birth.
This section includes distinct codes for specific defects, such as Q55.0 for absence and aplasia of the testis, using synonyms like agenesis of testis or anorchid azoospermia, which clarify coding for cases of missing or undeveloped testes. Code Q55.1 describes hypoplasia of testis and scrotum, linked to terms like Leydig cell hypoplasia and male infertility of developmental origin. Other codes address conditions like polyorchism (Q55.21), retractile testis (Q55.22), scrotal transposition (Q55.23), and various congenital malformations of the penis including curvature and hypoplasia (Q55.61–Q55.69). Codes such as Q55.3 and Q55.4 cover atresia and other malformations of the vas deferens, epididymis, and prostate. This classification guides clear identification and coding of specific male genital congenital anomalies, essential for precise documentation and management.
Questions About This Page
How many billable codes are in the Q55 range?
Of the 21 codes in this range, 18 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q55 range classify?
The range classifies other congenital malformations of male genital organs. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
