Other congenital malformations of female genitalia (Q52) ICD-10-CM
The Q52 code range covers other congenital malformations of female genitalia with 23 ICD-10-CM diagnosis codes. 19 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q52 Range 23 codes · 19 billable
- Q52 Other congenital malformations of female genitaliaNon-billable
- Q52.0 Congenital absence of vagina
- Q52.1 Doubling of vaginaNon-billable
- Q52.10 Doubling of vagina, unspecified
- Q52.11 Transverse vaginal septum
- Q52.12 Longitudinal vaginal septumNon-billable
- Q52.120 Longitudinal vaginal septum, nonobstructing
- Q52.121 Longitudinal vaginal septum, obstructing, right side
- Q52.122 Longitudinal vaginal septum, obstructing, left side
- Q52.123 Longitudinal vaginal septum, microperforate, right side
- Q52.124 Longitudinal vaginal septum, microperforate, left side
- Q52.129 Other and unspecified longitudinal vaginal septum
- Q52.2 Congenital rectovaginal fistula
- Q52.3 Imperforate hymen
- Q52.4 Other congenital malformations of vagina
- Q52.5 Fusion of labia
- Q52.6 Congenital malformation of clitoris
- Q52.7 Other and unspecified congenital malformations of vulvaNon-billable
- Q52.70 Unspecified congenital malformations of vulva
- Q52.71 Congenital absence of vulva
- Q52.79 Other congenital malformations of vulva
- Q52.8 Other specified congenital malformations of female genitalia
- Q52.9 Congenital malformation of female genitalia, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q52 range.
Arachnodactyly
An abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. Arachnodactyly can include feet and toes. Arachnodactyly has been associated with several gene mutations and syndromes.
Bicornuate Uterus
A congenital uterine anomaly in which the UTERUS is divided into two uterine horns with a significant cleft at the uterine fundus due to partial fusion of the MULLERIAN DUCTS. Bicornuate uterus is sometimes associated with a longitudinal vaginal septum and abnormal development of renal tracts.
Rectovaginal Fistula
An abnormal anatomical passage between the RECTUM and the VAGINA.
WAGR Syndrome
A contiguous gene syndrome associated with hemizygous deletions of chromosome region 11p13. The condition is marked by the combination of WILMS TUMOR; ANIRIDIA; GENITOURINARY ABNORMALITIES; and INTELLECTUAL DISABILITY.
About the Q52 Code Range
The ICD-10 code section Q52 covers various other congenital malformations of female genitalia, including rare structural differences present from birth. These codes are specifically used to identify and classify anomalies such as absence or duplication of the vagina, septal abnormalities, and malformations of the vulva and clitoris.
For example, Q52.0 refers to the congenital absence of vagina, also known as Mayer-Rokitansky-Küster-Hauser syndrome, a condition where the vagina and sometimes uterus are missing. Code Q52.1 relates to vaginal doubling, which includes septate vagina variants such as transverse (Q52.11) or longitudinal vaginal septum (Q52.12). Additionally, Q52.2 is used for congenital rectovaginal fistula, an abnormal fistulous connection between the rectum and vagina. Other malformations in this series address conditions like imperforate hymen (Q52.3), labial fusion (Q52.5), and various vulvar abnormalities (Q52.7 codes). The section aids in precise medical coding for congenital female genital tract anomalies to support accurate diagnosis and care documentation.
Questions About This Page
How many billable codes are in the Q52 range?
Of the 23 codes in this range, 19 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q52 range classify?
The range classifies other congenital malformations of female genitalia. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
