Indeterminate sex and pseudohermaphroditism (Q56) ICD-10-CM
The Q56 code range covers indeterminate sex and pseudohermaphroditism with 6 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q56 Range 6 codes · 5 billable
- Q56 Indeterminate sex and pseudohermaphroditismNon-billable
- Q56.0 Hermaphroditism, not elsewhere classified
- Q56.1 Male pseudohermaphroditism, not elsewhere classified
- Q56.2 Female pseudohermaphroditism, not elsewhere classified
- Q56.3 Pseudohermaphroditism, unspecified
- Q56.4 Indeterminate sex, unspecified
About the Q56 Code Range
ICD-10 code Q56 covers conditions involving indeterminate sex and pseudohermaphroditism, which are congenital anomalies where the physical or genetic sex characteristics are ambiguous or atypical. These codes classify disorders like hermaphroditism and male or female pseudohermaphroditism, helping guide medical documentation and diagnosis.
This section includes specific codes to distinguish between different forms of sex development disorders. For example, Q56.0 refers to hermaphroditism, also known as ovotesticular disorder of sex development or "false hermaphrodite," where individuals have both ovarian and testicular tissue. Q56.1 codes male pseudohermaphroditism, linked to various conditions such as partial gonadal dysgenesis and adrenal enzyme deficiencies in genetically male (46,XY) individuals. Similarly, Q56.2 pertains to female pseudohermaphroditism, describing cases involving ambiguous genitalia or sex development disorders in genetically female (46,XX) individuals, sometimes associated with maternal tumor influences. Other codes like Q56.3 and Q56.4 cover unspecified pseudohermaphroditism and indeterminate sex, respectively, to capture less defined presentations such as ambiguous genitalia. Medical coders seeking the ICD-10 code for ambiguous genitalia or related disorders will find the Q56 category essential for accurate classification.
Questions About This Page
How many billable codes are in the Q56 range?
Of the 6 codes in this range, 5 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q56 range classify?
The range classifies indeterminate sex and pseudohermaphroditism. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
