Congenital malformations of uterus and cervix (Q51)

ICD-10 code Q51 covers congenital malformations of the uterus and cervix, identifying specific developmental abnormalities present from birth. These codes are vital for coding conditions such as absence, duplication, or abnormal formation of uterine and cervical structures.

This section includes individual codes for various congenital uterine malformations like Q51.0, representing agenesis and aplasia of the uterus, also known by terms such as Mayer Rokitansky Küster Hauser syndrome type 1 or congenital absence of uterus. Codes Q51.10 and Q51.11 denote doubling of uterus with cervical and vaginal duplication, distinguished by obstruction presence or absence. Other specific forms include the bicornate uterus (Q51.3), unicornate uterus (Q51.4), and hypoplasia of uterus or cervix (Q51.811, Q51.821). The code cluster also identifies rarer conditions such as embryonic cysts of the cervix (Q51.6) and congenital fistulae between the uterus and digestive or urinary tracts (Q51.7). When the exact malformation is unspecified, Q51.9 is used. These codes help health professionals and coders document and communicate specific congenital uterine and cervical anomalies accurately.

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Bicornuate Uterus

A congenital uterine anomaly in which the UTERUS is divided into two uterine horns with a significant cleft at the uterine fundus due to partial fusion of the MULLERIAN DUCTS. Bicornuate uterus is sometimes associated with a longitudinal vaginal septum and abnormal development of renal tracts.