2027 ICD-10-CM Diagnosis Code Q56Indeterminate sex and pseudohermaphroditism

ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q56

ICD-10-CM Q56
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q56 is a non-billable ICD-10-CM category code for indeterminate sex and pseudohermaphroditism, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q56.0, Q56.1, Q56.2, and Q56.3.

Code Identity

ICD-10-CM Code
Q56
Billable Status
No — Non-Billable Category
Code Describes
Indeterminate sex and pseudohermaphroditism
Short Description
Indeterminate sex and pseudohermaphroditism
Same as the full description in the CMS dataset.
Chapter
Q50-Q56
Congenital malformations of genital organs

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ50-Q56Congenital malformations of genital organs
CategoryQ56Indeterminate sex and pseudohermaphroditism
This CodeQ56Indeterminate sex and pseudohermaphroditism

Specific Coding for Indeterminate sex and pseudohermaphroditismOverview

Non-specific codes like Q56 require more characters. Use one of these billable codes instead:

  • Use Q56.0 for Hermaphroditism, not elsewhere classified

  • Use Q56.1 for Male pseudohermaphroditism, not elsewhere classified

  • Use Q56.2 for Female pseudohermaphroditism, not elsewhere classified

  • Use Q56.3 for Pseudohermaphroditism, unspecified

  • Use Q56.4 for Indeterminate sex, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q56: its own notes plus those printed at block Q50-Q56 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

On Q56 itself
  • 46,XX true hermaphrodite (Q99.1)
  • androgen insensitivity syndrome (E34.5-)
  • chimera 46,XX/46,XY true hermaphrodite (Q99.0)
  • female pseudohermaphroditism with adrenocortical disorder (E25.-)
  • pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
  • pure gonadal dysgenesis (Q99.1)
From Block Q50-Q56 Congenital malformations of genital organs applies to 91 codes
  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q56, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q56: they are not reported together with it, unless the two conditions are unrelated.

  • E25 Adrenogenital disorders
    indeterminate sex and pseudohermaphroditism (Q56)

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Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q56Overview

What is the ICD-10 code for indeterminate sex and pseudohermaphroditism?

Q56 is the ICD-10-CM category for indeterminate sex and pseudohermaphroditism, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q56 (Indeterminate sex and pseudohermaphroditism) a billable code?

No. This is a category header that groups the codes for indeterminate sex and pseudohermaphroditism, and headers cannot be submitted on claims. Claims for indeterminate sex and pseudohermaphroditism need a more specific code from this category, such as Q56.0, Q56.1, and Q56.2.

Can Q56 be reported with Q99.1?

Not as a rule. The Excludes1 note on Q56 lists "46,XX true hermaphrodite (Q99.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).