2026 ICD-10-CM Diagnosis Code Q39.5Congenital dilatation of esophagus

ICD-10-CM CodesQ00-Q99Q38-Q45Q39

ICD-10-CM Q39.5
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q39.5 is a billable ICD-10-CM diagnosis code for congenital dilatation of esophagus. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 368 through 370. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q39.5
Billable Status
Yes — Valid for Submission
Code Describes
Congenital dilatation of esophagus
Short Description
Congenital dilatation of esophagus
Same as the full description in the CMS dataset.
Parent Code
Congenital malformations of esophagus

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ39Congenital malformations of esophagus
This CodeQ39.5Congenital dilatation of esophagus

Present on Admission (POA)Billing

Q39.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Achalasia microcephaly syndrome
  • Achalasia of esophagus
  • Alacrima
  • Complete deafness
  • Congenital achalasia of esophagus
  • Congenital anomaly of lacrimal gland
  • Congenital cardiospasm
  • Congenital deafness
  • Congenital dilatation of esophagus
  • Congenital stenosis of esophagus
  • Congenital stenosis of stomach
  • Deafness, vitiligo, achalasia syndrome
  • Dilatation of esophagus
  • Giant esophagus
  • Intellectual disability, alacrima, achalasia syndrome
  • Stricture of esophagus

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital cardiospasm

Index to Diseases and InjuriesGuidance

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Achalasia(cardia) (esophagus)
      • congenital
    • Cardiospasm(esophagus) (reflex) (stomach)
      • congenital
    • Cardiospasm(esophagus) (reflex) (stomach)
      • congenital
        • with megaesophagus
    • Dilatation
      • esophagus
        • congenital
    • Giant
      • esophagus, congenital
    • Megaesophagus(functional)
      • congenital
    • Megaloesophagus(functional)
      • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q39.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
750.4 Esophageal anomaly NEC
Approximate The match is approximate rather than exact.
ICD-9-CM
750.7 Gastric anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q39.5Overview

Is Q39.5 (Congenital malformations of esophagus) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital dilatation of esophagus on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q39.5 group to?

When congenital dilatation of esophagus is the principal diagnosis on an inpatient stay, it groups to MS-DRG 368, 369, 370, with relative weights from 0.7008 to 1.5919 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q39.5 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital dilatation of esophagus on inpatient claims.

What is the ICD-9 equivalent of Q39.5?

Under the General Equivalence Mappings, congenital dilatation of esophagus converts to ICD-9-CM 750.4 (esophageal anomaly NEC) and 750.7 (gastric anomaly NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.