2024 ICD-10-CM Diagnosis Code K22.0

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Absent peristalsis
• Achalasia
• Achalasia due to Chagas disease
• Achalasia of esophagus
• Achalasia of esophagus
• Achalasia of esophagus
• Achalasia of esophagus
• Acquired achalasia of esophagus
• Acquired achalasia of esophagus
• Adrenocorticotropic hormone resistance syndrome
• Aperistalsis of esophagus
• Congenital achalasia of esophagus
• Dilatation of esophagus
• Dilatation of esophagus
• Disorder of esophageal peristalsis
• Glucocorticoid deficiency with achalasia
• Hypertensive spasm of cardiac sphincter
• Idiopathic achalasia of esophagus
• Idiopathic megaesophagus
• Megaesophagus
• Moyamoya disease
• Moyamoya disease with early onset achalasia
• Pituitary thyroid hormone resistance
• Primary adrenocortical insufficiency
• Thyroid hormone resistance syndrome

Clinical Information

• Thyroid Hormone Resistance Syndrome-. an inherited autosomal recessive trait, characterized by peripheral resistance to thyroid hormones and the resulting elevation in serum levels of thyroxine and triiodothyronine. this syndrome is caused by mutations of gene thrb encoding the thyroid hormone receptors beta in target cells. hypothyroidism in these patients is partly overcome by the increased thyroid hormone levels.
• Moyamoya Disease-. a noninflammatory, progressive occlusion of the intracranial carotid arteries and the formation of netlike collateral arteries arising from the circle of willis. cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. it is characterized by endothelial hyperplasia and fibrosis with thickening of arterial walls. this disease primarily affects children but can also occur in adults.
• AAAS wt Allele|AAA|AAASb|ADRACALA|ADRACALIN|ALADIN|Achalasia, Adrenocortical Insufficiency, Alacrimia (Allgrove, Triple-A) Gene|Achalasia, Adrenocortical Insufficiency, Alacrimia Gene|Aladin WD Repeat Nucleoporin wt Allele|Allgrove, Triple-A Gene|GL003-. human aaas wild-type allele is located in the vicinity of 12q13.13 and is approximately 17 kb in length. this allele, which encodes aladin protein, is involved in peripheral and central nervous system development and mitotic spindle formation. mutations in the gene are associated with achalasia-addisonianism-alacrima syndrome (allgrove or triple-a syndrome).
• Achalasia-. failure of the smooth muscle fibers of the gastrointestinal tract to relax at any one point of junction of one part with another.
• Esophageal Achalasia|Achalasia Cardia|Achalasia of Cardia-. a finding indicating the lack of adequate relaxation of the lower esophageal sphincter resulting in difficulty swallowing food.
• Triple A Syndrome|3A syndrome|Achalasia-Addisonianism-Alacrima Syndrome|Allgrove Syndrome|Allgrove Syndrome|Triple-A syndrome-. an autosomal recessive condition caused by mutation(s) in the aaas gene encoding the protein aladin, and characterized by primary adrenal insufficiency, esophageal dysmotility, and absence of tear production.
• Moyamoya Disease-. a rare inherited vascular disorder characterized by constriction of arteries at the base of the brain, resulting in the formation of collateral circulation in order to compensate for the constriction. the name "moyamoya" in japanese means "puff of smoke" and derives from the characteristic radiographic appearance of the collateral vessels.
• Moyamoya Disease 2|MYMY2-. an autosomally inherited subtype of moyamoya disease often presenting in childhood caused by mutation(s) in the rnf213 gene, encoding e3 ubiquitin-protein ligase rnf213.
• RNF213 wt Allele|ALK Lymphoma Oligomerization Partner on Chromosome 17 Gene|ALO17|C17orf27|Chromosome 17 Open Reading Frame 27 Gene|DKFZp762N1115|FLJ13051|KIAA1554|KIAA1618|MGC46622|MGC9929|MYMY2|MYSTR|Moyamoya Disease 2 Gene|NET57|Ring Finger Protein 213 wt Allele|hCG_1812857-. human rnf213 wild-type allele is located in the vicinity of 17q25.3 and is approximately 135 kb in length. this allele, which encodes e3 ubiquitin-protein ligase rnf213 protein, may play a role in the regulation of protein ubiquitination. a chromosomal translocation t(2;17)(p23;q25) of this gene with the alk gene is associated with anaplastic large cell lymphoma.
• Megaesophagus-. an abnormal dilation of the esophagus not due to obstruction.

Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
391	ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITH MCC	06	1.2757
392	ESOPHAGITIS, GASTROENTERITIS AND MISCELLANEOUS DIGESTIVE DISORDERS WITHOUT MCC	06	0.7856

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Convert to ICD-9-CM Code

Source ICD-10-CM Code		Target ICD-9-CM Code
K22.0		530.0 - Achalasia & cardiospasm
Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education

Esophagus Disorders

The esophagus is the muscular tube that carries food and liquids from your mouth to the stomach. You may not be aware of your esophagus until you swallow something too large, too hot, or too cold. You may also notice it when something is wrong. You may feel pain or have trouble swallowing.

The most common problem with the esophagus is GERD (gastroesophageal reflux disease). With GERD, a muscle at the end of your esophagus does not close properly. This allows stomach contents to leak back, or reflux, into the esophagus and irritate it. Over time, GERD can cause damage to the esophagus.

Other problems include heartburn, cancer, and eosinophilic esophagitis. Doctors may use various tests to make a diagnosis. These include imaging tests, an upper endoscopy, and a biopsy.

Treatment depends on the problem. Some problems get better with over-the-counter medicines or changes in diet. Others may need prescription medicines or surgery.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

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Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.