2026 ICD-10-CM Diagnosis Code Q28.2Arteriovenous malformation of cerebral vessels

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q28

ICD-10-CM Q28.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q28.2 is a billable ICD-10-CM diagnosis code for arteriovenous malformation of cerebral vessels. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q28.2
Billable Status
Yes — Valid for Submission
Code Describes
Arteriovenous malformation of cerebral vessels
Short Description
Arteriovenous malformation of cerebral vessels
Same as the full description in the CMS dataset.
Parent Code
Q28
Other congenital malformations of circulatory system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ28Other congenital malformations of circulatory system
This CodeQ28.2Arteriovenous malformation of cerebral vessels

Present on Admission (POA)Billing

Q28.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arteriovenous fistula of great cerebral vein of Galen
  • Cerebral arteriovenous malformation
  • Cerebrofacial arteriovenous metameric syndrome
  • Cerebrofacial arteriovenous metameric syndrome type 1
  • Cerebrofacial arteriovenous metameric syndrome type 2
  • Cerebrofacial arteriovenous metameric syndrome type 3
  • Congenital arteriovenous fistula of brain
  • Congenital cerebral arteriovenous aneurysm
  • Edema of foot
  • Hemichorea
  • Hemichorea due to cerebral arteriovenous malformation
  • Lymphedema and cerebral arteriovenous anomaly syndrome
  • Lymphedema of lower extremity
  • Ruptured cerebral arteriovenous malformation
  • Vein of Galen malformation

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Arteriovenous malformation of brain NOS
  • Congenital arteriovenous cerebral aneurysm (nonruptured)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • arteriovenous (congenital)
        • brain
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • brain
        • arteriovenous (congenital) (nonruptured)
    • Fistula(cutaneous)
      • arteriovenous (acquired) (nonruptured)
        • brain
          • congenital
    • Fistula(cutaneous)
      • arteriovenous (acquired) (nonruptured)
        • congenital (peripheral)
          • brain
    • Fistula(cutaneous)
      • brain
        • arteriovenous (acquired)
          • congenital
    • Malformation(congenital)
      • arteriovenous, aneurysmatic (congenital)
        • brain
    • Malformation(congenital)
      • arteriovenous, aneurysmatic (congenital)
        • cerebral
    • Malformation(congenital)
      • brain (multiple)
        • arteriovenous

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Vein of Galen Malformation

    an arteriovenous malformation in the vein of galen that is located at the base of the brain. the malformation may result in developmental delays, hydrocephalus, seizures, and congestive heart failure.

Patient EducationClinical

Arteriovenous Malformations

Arteriovenous malformations (AVMs) are defects in your vascular system. Your vascular system is your body's network of blood vessels. It includes your:

The full article covers:

  • What are arteriovenous malformations (AVMs)?
  • What causes arteriovenous malformations (AVMs)?
  • What are the symptoms of arteriovenous malformations (AVMs)?
  • How are arteriovenous malformations (AVMs) diagnosed?
  • What are the treatments for arteriovenous malformations (AVMs)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q28.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.81 Cerebrovascular anomaly
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q28.2Overview

Is Q28.2 (Other congenital malformations of circulatory system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report arteriovenous malformation of cerebral vessels on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Is Q28.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for arteriovenous malformation of cerebral vessels on inpatient claims.

What is the ICD-9 equivalent of Q28.2?

Under the General Equivalence Mappings, arteriovenous malformation of cerebral vessels converts to ICD-9-CM 747.81 (cerebrovascular anomaly). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.