2027 ICD-10-CM Diagnosis Code Q27.1Congenital renal artery stenosis

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q27.1 is a billable ICD-10-CM diagnosis code for congenital renal artery stenosis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. Coders also document this condition as bilateral congenital anomaly of renal arteries. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.1
Billable Status
Yes — Valid for Submission
Code Describes
Congenital renal artery stenosis
Short Description
Congenital renal artery stenosis
Same as the full description in the CMS dataset.
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.1Congenital renal artery stenosis

Present on Admission (POA)Billing

Q27.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral congenital anomaly of renal arteries
  • Bilateral congenital stenosis of renal arteries
  • Bilateral renal artery stenosis
  • Congenital anomaly of left renal artery
  • Congenital anomaly of right renal artery
  • Congenital renal artery stenosis
  • Congenital stenosis of left renal artery
  • Congenital stenosis of right renal artery
  • Stenosis of left renal artery
  • Stenosis of right renal artery

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q27.1: its own notes plus those printed at Q27 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Q27 Other congenital malformations of peripheral vascular system applies to 12 codes
  • anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
  • anomalies of coronary vessels (Q24.5)
  • anomalies of pulmonary artery (Q25.5-Q25.7)
  • congenital retinal aneurysm (Q14.1)
  • hemangioma and lymphangioma (D18.-)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q27.1, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q27.1: they are not reported together with it, unless the two conditions are unrelated.

  • N28.0 Ischemia and infarction of kidney
    congenital stenosis of renal artery (Q27.1)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.62 Renal vessel anomaly
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q27.1Overview

What is the ICD-10 code for congenital renal artery stenosis?

The ICD-10-CM code for congenital renal artery stenosis is Q27.1 (sometimes written as Q271). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q27.1 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital renal artery stenosis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q27.1 group to?

When congenital renal artery stenosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 301, 300, 299, with relative weights from 0.7132 to 1.5840 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital renal artery stenosis on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.

What is the ICD-9 equivalent of Q27.1?

Under the General Equivalence Mappings, congenital renal artery stenosis converts to ICD-9-CM 747.62 (renal vessel anomaly). The mapping is approximate, so confirm the match fits the documentation.