2026 ICD-10-CM Diagnosis Code Q27.1Congenital renal artery stenosis

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q27.1 is a billable ICD-10-CM diagnosis code for congenital renal artery stenosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.1
Billable Status
Yes — Valid for Submission
Code Describes
Congenital renal artery stenosis
Short Description
Congenital renal artery stenosis
Same as the full description in the CMS dataset.
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.1Congenital renal artery stenosis

Present on Admission (POA)Billing

Q27.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral congenital anomaly of renal arteries
  • Bilateral congenital stenosis of renal arteries
  • Bilateral renal artery stenosis
  • Congenital anomaly of left renal artery
  • Congenital anomaly of right renal artery
  • Congenital renal artery stenosis
  • Congenital stenosis of left renal artery
  • Congenital stenosis of right renal artery
  • Stenosis of left renal artery
  • Stenosis of right renal artery

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Stenosis, stenotic(cicatricial)
      • renal artery
        • congenital
    • Stricture
      • renal artery
        • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
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Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.62 Renal vessel anomaly
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q27.1Overview

Is Q27.1 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital renal artery stenosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q27.1 group to?

When congenital renal artery stenosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital renal artery stenosis on inpatient claims.

What is the ICD-9 equivalent of Q27.1?

Under the General Equivalence Mappings, congenital renal artery stenosis converts to ICD-9-CM 747.62 (renal vessel anomaly). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.