2027 ICD-10-CM Diagnosis Code Q18.9Congenital malformation of face and neck, unspecified
ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q18
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q18.9 is a billable ICD-10-CM diagnosis code for congenital malformation of face and neck, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q18.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of eye, ear, face and neck (Q10-Q18).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Autosomal recessive facio-digito-genital syndrome
- Bone age finding
- Brachymesophalangia
- CDK13-related congenital heart defects, intellectual disability, facial dysmorphism syndrome
- Cerebrofacial dysplasia
- Congenital anomaly of anterior portion of neck
- Congenital anomaly of face
- Congenital anomaly of neck
- Congenital cataracts, facial dysmorphism and neuropathy
- Congenital deformity of face
- Congenital fusion of kidneys
- Congenital malformation of eye, ear and neck
- Craniosynostosis, facial dysmorphism, Chiari-1 malformation, developmental and language delay syndrome
- Deafness craniofacial syndrome
- Delayed bone age
- Developmental delay, overweight, facial dysmorphism, behavioral abnormalities syndrome
- Disorder of ornithine metabolism
- Dysmorphic facies
- Dysmorphic features
- Ear, face and neck congenital anomalies
- Essential tremor
- Faciocardiorenal syndrome
- Familial visceral neuropathy
- Gingival fibromatosis
- Gingival fibromatosis with facial dysmorphism syndrome
- Global developmental delay, alopecia, macrocephaly, facial dysmorphism, structural brain anomalies syndrome
- Hereditary essential tremor
- Hereditary gingival fibromatosis
- Heritable disorder of neutrophil function
- Horseshoe kidney
- Intellectual disability, muscle weakness, short stature, facial dysmorphism syndrome
- Loose anagen hair syndrome
- Macrothrombocytopenia, lymphedema, developmental delay, facial dysmorphism, camptodactyly syndrome
- Megakaryocytic thrombocytopenia
- Microcephaly, corpus callosum hypoplasia, intellectual disability, facial dysmorphism syndrome
- Multiple malformation syndrome, moderate short stature, facial
- Neurofaciodigitorenal syndrome
- Noonan syndrome-like disorder with loose anagen hair
- Oral-facial-digital syndrome with short stature and brachymesophalangia
- Oro-facial digital syndrome type 9
- Otofaciocervical syndrome
- Otospondylomegaepiphyseal dysplasia
- Palatal anomalies, widely spaced teeth, facial dysmorphism, developmental delay syndrome
- PHIP-related behavioral problems, intellectual disability, obesity, dysmorphic features syndrome
- Progressive essential tremor, speech impairment, facial dysmorphism, intellectual disability, abnormal behavior syndrome
- Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
- Severe intellectual disability, agenesis of corpus callosum, facial dysmorphism, cerebellar ataxia syndrome
- Short stature with valvular heart disease and characteristic facies syndrome
- Structural abnormality of Auerbach plexus
- Thong Douglas Ferrante syndrome
- TRAF7-associated heart defect, digital anomalies, facial dysmorphism, motor and speech delay syndrome
- Trichorhinophalangeal syndrome
- Trichorhinophalangeal syndrome type 1 and 3
- Visceral neuropathy and brain anomaly with facial dysmorphism and developmental delay syndrome
- X-linked external auditory canal atresia, dilated internal auditory canal, facial dysmorphism syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q18.9: its own notes plus those printed at Q18, block Q10-Q18, and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Congenital anomaly NOS of face and neck
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- cleft lip and cleft palate (Q35-Q37)
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
- congenital malformation of larynx (Q31.-)
- congenital malformation of lip NEC (Q38.0)
- congenital malformation of nose (Q30.-)
- congenital malformation of parathyroid gland (Q89.2)
- congenital malformation of thyroid gland (Q89.2)
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q18.9, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Anomaly, anomalous (congenital) (unspecified type) Q89.9
cheek Q18.9
chin Q18.9
face Q18.9
neck (any part) Q18.9
congenital Q18.9
congenital Q18.9
congenital Q18.9
congenital Q18.9
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Craniofacial Abnormalities
Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q18.9 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q18.9Overview
What is the ICD-10 code for congenital malformation of face and neck, unspecified?
The ICD-10-CM code for congenital malformation of face and neck, unspecified is Q18.9 (sometimes written as Q189). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q18.9 (Other congenital malformations of face and neck) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of face and neck, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q18.9 group to?
When congenital malformation of face and neck, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q18.9 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of face and neck, unspecified on inpatient claims. The code appears in the Congenital malformations of eye, ear, face and neck (Q10-Q18) range of the CMS exempt list.
Can Q18.9 be reported with a code from Q75?
Not as a rule. The Excludes1 note at Q18, which applies to Q18.9, lists "congenital malformations of skull and face bones (Q75.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
