2026 ICD-10-CM Diagnosis Code Q13.1Absence of iris

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13

ICD-10-CM Q13.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q13.1 is a billable ICD-10-CM diagnosis code for absence of iris. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q13.1
Billable Status
Yes — Valid for Submission
Code Describes
Absence of iris
Short Description
Absence of iris
Same as the full description in the CMS dataset.
Parent Code
Q13
Congenital malformations of anterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ13Congenital malformations of anterior segment of eye
This CodeQ13.1Absence of iris

Present on Admission (POA)Billing

Q13.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 11p partial monosomy syndrome
  • Aniridia and absent patella syndrome
  • Aniridia and intellectual disability syndrome
  • Aniridia type 1
  • Aniridia type 2
  • Aniridia, ptosis, intellectual disability, familial obesity syndrome
  • Aniridia, renal agenesis, psychomotor retardation syndrome
  • Bilateral congenital aniridia of eyes
  • Congenital aniridia
  • Congenital aniridia of left eye
  • Congenital aniridia of right eye
  • Congenital anomaly of patella
  • Deletion of part of chromosome 11
  • Renal agenesis
  • WAGR syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Aniridia

Use Additional Code

  • code for associated glaucoma H42

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • iris, congenital
    • Agenesis
      • iris (dilator fibers)
    • Aniridia(congenital)
    • Aplasia
      • iris
    • Glaucoma
      • in (due to)
        • aniridia
    • Irideremia

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • WAGR Syndrome

    a contiguous gene syndrome associated with hemizygous deletions of chromosome region 11p13. the condition is marked by the combination of wilms tumor; aniridia; genitourinary abnormalities; and intellectual disability.

  • Bilateral Renal Agenesis

    a congenital abnormality characterized by the absence of both kidneys.

  • Renal Agenesis

    a congenital abnormality characterized by the absence of one or both kidneys.

  • Unilateral Renal Agenesis|Congenital Single Kidney|Congenital Solitary Kidney|Congenital Solitary Kidney

    a congenital abnormality characterized by the presence of only one kidney.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q13.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.45 Aniridia
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q13.1Overview

Is Q13.1 (Congenital malformations of anterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report absence of iris on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q13.1 group to?

When absence of iris is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q13.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for absence of iris on inpatient claims.

What is the ICD-9 equivalent of Q13.1?

Under the General Equivalence Mappings, absence of iris converts to ICD-9-CM 743.45 (aniridia). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.