2027 ICD-10-CM Diagnosis Code Q13.0Coloboma of iris
ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q13.0 is a billable ICD-10-CM diagnosis code for coloboma of iris. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q13.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of eye, ear, face and neck (Q10-Q18).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Abruzzo Erickson syndrome
- Agenesis of corpus callosum, intellectual disability, coloboma, micrognathia syndrome
- Atresia of nasolacrimal duct
- Biemond syndrome type 2
- Bilateral microphthalmos
- Bilateral microphthalmos with congenital coloboma
- Central obesity
- Coloboma of eye
- Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome
- Colobomatous macrophthalmia with microcornea syndrome
- Colobomatous microphthalmia
- Colobomatous microphthalmia, obesity, hypogenitalism, intellectual disability syndrome
- COMMAD syndrome
- Complete deafness
- Congenital coloboma of bilateral irides
- Congenital coloboma of iris
- Congenital coloboma of iris of left eye
- Congenital coloboma of iris of right eye
- Congenital coloboma of optic disc
- Congenital deafness
- Congenital mixed conductive and sensorineural hearing loss
- Familial progressive retinal dystrophy, iris coloboma, congenital cataract syndrome
- Fundus coloboma
- Macrophthalmos
- Microcornea
- Microphthalmos of left eye
- Microphthalmos of right eye
- Microtia
- Microtia, eye coloboma, imperforation of nasolacrimal duct syndrome
- Mixed conductive AND sensorineural hearing loss
- Preaxial polydactyly, colobomata, intellectual disability syndrome
- Progressive macrocephaly
- Renal coloboma syndrome
- Temtamy syndrome
- Uveal coloboma with cleft lip and palate and intellectual disability syndrome
- X-linked cerebral, cerebellar, coloboma syndrome
- X-linked sensorineural hearing loss
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q13.0: its own notes plus those printed at block Q10-Q18 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Coloboma NOS
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- cleft lip and cleft palate (Q35-Q37)
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
- congenital malformation of larynx (Q31.-)
- congenital malformation of lip NEC (Q38.0)
- congenital malformation of nose (Q30.-)
- congenital malformation of parathyroid gland (Q89.2)
- congenital malformation of thyroid gland (Q89.2)
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Coloboma (iris) Q13.0
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Coloboma
congenital anomaly in which some of the structures of the eye are absent due to incomplete fusion of the fetal intraocular fissure during gestation.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q13.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q13.0Overview
What is the ICD-10 code for coloboma of iris?
The ICD-10-CM code for coloboma of iris is Q13.0 (sometimes written as Q130). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q13.0 (Congenital malformations of anterior segment of eye) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report coloboma of iris on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q13.0 group to?
When coloboma of iris is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q13.0 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for coloboma of iris on inpatient claims. The code appears in the Congenital malformations of eye, ear, face and neck (Q10-Q18) range of the CMS exempt list.
What is the ICD-9 equivalent of Q13.0?
Under the General Equivalence Mappings, coloboma of iris converts to ICD-9-CM 743.46 (anom iris & cil body NEC). The mapping is approximate, so confirm the match fits the documentation.
