2026 ICD-10-CM Diagnosis Code N07.8Hereditary nephropathy, not elsewhere classified with other morphologic lesions

ICD-10-CM Codes›N00–N99›N00-N08›N07

ICD-10-CM N07.8
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N07.8 is a billable ICD-10-CM diagnosis code for hereditary nephropathy, not elsewhere classified with other morphologic lesions. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. Coders also document this condition as fibronectin glomerulopathy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nephritis; nephrosis; renal sclerosis.

Code Identity

ICD-10-CM Code
N07.8
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary nephropathy, not elsewhere classified with other morphologic lesions
Short Description
Hereditary nephropathy, NEC w oth morphologic lesions
Parent Code
N07
Hereditary nephropathy, not elsewhere classified

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN07Hereditary nephropathy, not elsewhere classified
This CodeN07.8Hereditary nephropathy, not elsewhere classified with other morphologic lesions

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Fibronectin glomerulopathy
  • Gitelman-like kidney tubulopathy due to mitochondrial DNA mutation
  • Glomerulopathy with fibronectin deposits 1
  • Thyrocerebrorenal syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Hereditary nephropathy, not elsewhere classified with proliferative glomerulonephritis NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Nephropathy
      • hereditary NEC
        • with
          • specified morphological changes NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR GEN001
Nephritis; nephrosis; renal sclerosis
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Genetic Disorders

Genetic disorders are health conditions caused by changes (also called mutations or variants) in your genes. Genes are parts of DNA found in your cells that carry instructions for how your body grows, develops, and functions. Many genes tell your body how to make proteins, which are needed for your body to work properly.

The full article covers:

  • What are genetic disorders?
  • What causes genetic disorders?
  • What are the types of genetic disorders?
  • What are the different ways a genetic disorder can be inherited?
  • How are genetic disorders diagnosed?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert N07.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
583.89 Nephritis NEC
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replaced This code was replaced in the FY 2026 code set by:

  • N07.B - Hereditary nephrop, NEC with APOL1-mediated kidney disease
  • N07.B - Hereditary nephrop, NEC with APOL1-mediated kidney disease
FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About N07.8Overview

Is N07.8 (Hereditary nephropathy, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary nephropathy, not elsewhere classified with other morphologic lesions on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does N07.8 group to?

When hereditary nephropathy, not elsewhere classified with other morphologic lesions is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of N07.8?

Under the General Equivalence Mappings, hereditary nephropathy, not elsewhere classified with other morphologic lesions converts to ICD-9-CM 583.89 (nephritis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.