2026 ICD-10-CM Diagnosis Code N04.ANephrotic syndrome with C3 glomerulonephritis

ICD-10-CM Codes›N00–N99›N00-N08›N04

ICD-10-CM N04.A
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N04.A is a billable ICD-10-CM diagnosis code for nephrotic syndrome with C3 glomerulonephritis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nephritis; nephrosis; renal sclerosis.

Code Identity

ICD-10-CM Code
N04.A
Billable Status
Yes — Valid for Submission
Code Describes
Nephrotic syndrome with C3 glomerulonephritis
Short Description
Nephrotic syndrome with C3 glomerulonephritis
Same as the full description in the CMS dataset.
Parent Code
N04
Nephrotic syndrome

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN04Nephrotic syndrome
This CodeN04.ANephrotic syndrome with C3 glomerulonephritis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Nephrotic syndrome with C3 glomerulopathy

Type 1 Excludes

  • Nephrotic syndrome with C3 glomerulopathy with dense deposit disease N04.6

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • nephrotic (congenital)
        • with
          • C3
            • glomerulonephritis
    • Syndrome
      • nephrotic (congenital)
        • with
          • C3
            • glomerulopathy

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR GEN001
Nephritis; nephrosis; renal sclerosis
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Nephrosis, Lipoid

    a kidney disease with no or minimal histological glomerular changes on light microscopy and with no immune deposits. it is characterized by lipid accumulation in the epithelial cells of kidney tubules and in the urine. patients usually show nephrotic syndrome indicating the presence of proteinuria with accompanying edema.

  • Nephrotic Syndrome

    a condition characterized by severe proteinuria, greater than 3.5 g/day in an average adult. the substantial loss of protein in the urine results in complications such as hypoproteinemia; generalized edema; hypertension; and hyperlipidemias. diseases associated with nephrotic syndrome generally cause chronic kidney dysfunction.

Code History & ChangesHistory

Replacement N04.A replaces the following previously assigned code(s):

  • N04.8 - Nephrotic syndrome with other morphologic changes
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About N04.AOverview

Is N04.A (Nephrotic syndrome) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report nephrotic syndrome with C3 glomerulonephritis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does N04.A group to?

When nephrotic syndrome with C3 glomerulonephritis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.