ICD-10 Code N04.9

Nephrotic syndrome with unspecified morphologic changes

Version 2019 Billable Code

Valid for Submission

N04.9 is a billable code used to specify a medical diagnosis of nephrotic syndrome with unspecified morphologic changes. The code is valid for the year 2020 for the submission of HIPAA-covered transactions.

ICD-10: N04.9
Short Description:Nephrotic syndrome with unspecified morphologic changes
Long Description:Nephrotic syndrome with unspecified morphologic changes

Code Classification

  • Diseases of the genitourinary system (N00–N99)
    • Glomerular diseases (N00-N08)
      • Nephrotic syndrome (N04)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (first year ICD-10-CM implemented into the HIPAA mandated code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Medical Professionals

Diagnostic Related Groups

The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). The diagnosis code N04.9 is grouped in the following groups for version MS-DRG V37.0 applicable from 10/01/2020 through 09/30/2020.

  • 698 - OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH MCC
  • 699 - OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITH CC
  • 700 - OTHER KIDNEY AND URINARY TRACT DIAGNOSES WITHOUT CC/MCC

Convert N04.9 to ICD-9

The following crosswalk between ICD-10 to ICD-9 is based based on the General Equivalence Mappings (GEMS) information:

  • 581.9 - Nephrotic syndrome NOS (Approximate Flag)

Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Anasarca
  • Childhood nephrotic syndrome
  • Congenital nephrotic syndrome
  • Congenital nephrotic syndrome due to congenital infection
  • Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome
  • Disorder of kidney co-occurrent with human immunodeficiency virus infection
  • Epstein syndrome
  • Familial idiopathic steroid-resistant nephrotic syndrome
  • Galloway Mowat syndrome
  • LAMB2-related infantile-onset nephrotic syndrome
  • Megakaryocytic thrombocytopenia
  • Multi-drug resistant nephrotic syndrome
  • Nephritic syndrome
  • Nephrosis, deafness, urinary tract, digital malformation syndrome
  • Nephrotic syndrome
  • Nephrotic syndrome associated with another disorder
  • Nephrotic syndrome associated with another disorder
  • Nephrotic syndrome associated with another disorder
  • Nephrotic syndrome co-occurrent with human immunodeficiency virus infection
  • Nephrotic syndrome in amyloidosis
  • Nephrotic syndrome in malaria
  • Nephrotic syndrome in polyarteritis nodosa
  • Nephrotic syndrome secondary to glomerulonephritis
  • Nephrotic syndrome secondary to systemic disease
  • Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
  • Nephrotic-nephritic syndrome
  • Pierson syndrome
  • Pulmonic stenosis and congenital nephrosis
  • Renal anasarca
  • Renal hematuria
  • Sporadic idiopathic steroid-resistant nephrotic syndrome
  • Steroid resistant nephrotic syndrome of childhood
  • Steroid sensitive nephrotic syndrome of childhood
  • Steroid-dependent nephrotic syndrome
  • Steroid-resistant nephrotic syndrome
  • Steroid-resistant nephrotic syndrome
  • Steroid-sensitive nephrotic syndrome

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code N04.9 are found in the index:


Information for Patients


Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.

Most kidney diseases attack the nephrons. This damage may leave kidneys unable to remove wastes. Causes can include genetic problems, injuries, or medicines. You have a higher risk of kidney disease if you have diabetes, high blood pressure, or a close family member with kidney disease. Chronic kidney disease damages the nephrons slowly over several years. Other kidney problems include

  • Cancer
  • Cysts
  • Stones
  • Infections

Your doctor can do blood and urine tests to check if you have kidney disease. If your kidneys fail, you will need dialysis or a kidney transplant.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


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ICD-10 Footnotes

General Equivalence Map Definitions
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.