2024 ICD-10-CM Diagnosis Code N04.8
Nephrotic syndrome with other morphologic changes
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Congenital nephrotic syndrome
- Drash syndrome
- Finnish congenital nephrotic syndrome
- Glomerular disease due to Finnish type congenital nephrotic syndrome
- Nephrotic syndrome with proliferative glomerulonephritis
Clinical Category is Nephritis; nephrosis; renal sclerosis
- CCSR Category Code: GEN001
- Inpatient Default CCSR: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
- Outpatient Default CCSR: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.
Congenital Nephrotic Syndromea rare autosomal recessive inherited nephrotic syndrome that is present in the first week of life. it manifests with edema and proteinuria and usually has a poor prognosis.
Congenital Nephrotic Syndrome - Cytomegalovirus Associated|Cytomegalovirus Associated Congenital Nephrotic Syndromenephrotic syndrome associated with a cytomegalovirus infection, most commonly presenting in the first three months of life.
Congenital Nephrotic Syndrome - Diffuse Mesangial Sclerosis|Diffuse Mesangial Sclerosis|Diffuse Mesangial Sclerosisnephrotic syndrome within the first three motnhs of life, characterized initially by increased mesangial matrix, with or without hypertrophy and hyperplasia of podocytes, and eventual glomerular sclerosis.
Congenital Nephrotic Syndrome - Focal Segmental Glomerulosclerosis|Congenital FSGS|Congenital FSGSnephrotic syndrome within the first three months of life, characterized by scarring of the glomerulus, in which only part of the glomerulus is involved, and less than 50% of the glomeruli are affected.
Congenital Nephrotic Syndrome - Infection Associated|Infection Associated Congenital Nephrotic Syndromenephrotic syndrome presenting within the first three months of life, and which is associated with an infectious process.
Congenital Nephrotic Syndrome - Rubivirus Associated|Rubivirus Associated Congenital Nephrotic Syndromenephrotic syndrome associated with rubella, most commonly presenting in the first three months of life.
Congenital Nephrotic Syndrome - Toxoplasma Associated|Toxoplasma Associated Congenital Nephrotic Syndromenephrotic syndrome associated with toxoplasmosis, most commonly presenting in the first three months of life.
Congenital Nephrotic Syndrome - Treponema Pallidum Associated|Treponema Pallidum Associated Congenital Nephrotic Syndromenephrotic syndrome associated with syphilis, most commonly presenting in the first three months of life.
Nephrotic Syndrome - NPHS1 Associated|Congenital Nephrotic Syndrome - Finnish Typenephrotic syndrome attributed to mutation(s) in the nphs1 gene, which encodes the protein nephrin, and most commonly presents during the first three months of life.
Tabular List of Diseases and Injuries
The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.
Inclusion TermsInclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Nephrotic syndrome with proliferative glomerulonephritis NOS
Index to Diseases and Injuries References
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.
Most kidney diseases attack the nephrons. This damage may leave kidneys unable to remove wastes. Causes can include genetic problems, injuries, or medicines. You have a higher risk of kidney disease if you have diabetes, high blood pressure, or a close family member with kidney disease. Chronic kidney disease damages the nephrons slowly over several years. Other kidney problems include:
Your doctor can do blood and urine tests to check if you have kidney disease. If your kidneys fail, you will need dialysis or a kidney transplant.
NIH: National Institute of Diabetes and Digestive and Kidney Diseases
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- FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
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- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
 Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.