2026 ICD-10-CM Diagnosis Code M34.81Systemic sclerosis with lung involvement

ICD-10-CM Codes›M00–M99›M30-M36›M34

ICD-10-CM M34.81
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

M34.81 is a billable ICD-10-CM diagnosis code for systemic sclerosis with lung involvement. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. Coders also document this condition as lung disease with systemic sclerosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Systemic lupus erythematosus and connective tissue disorders.

Code Identity

ICD-10-CM Code
M34.81
Billable Status
Yes — Valid for Submission
Code Describes
Systemic sclerosis with lung involvement
Short Description
Systemic sclerosis with lung involvement
Same as the full description in the CMS dataset.
Parent Code
M34.8
Other forms of systemic sclerosis

Code Classification

ChapterM00–M99Diseases of the musculoskeletal system and connective tissue
SectionM30-M36Systemic connective tissue disorders
CategoryM34Systemic sclerosis [scleroderma]
This CodeM34.81Systemic sclerosis with lung involvement

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Lung disease with systemic sclerosis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Code Also

  • if applicable:
  • other interstitial pulmonary diseases J84.89
  • secondary pulmonary arterial hypertension I27.21

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • lung
        • in
          • systemic
            • sclerosis
    • Sclerosis, sclerotic
      • systemic
        • with
          • lung involvement

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MUS024
Systemic lupus erythematosus and connective tissue disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Lung Diseases

When you breathe, your lungs take in oxygen from the air and deliver it to the bloodstream. The cells in your body need oxygen to work and grow. During a normal day, you breathe nearly 25,000 times. People with lung disease have difficulty breathing. Millions of people in the U.S. have lung disease.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert M34.81 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
710.1 Systemic sclerosis
ApproximateCombination The match is approximate, and more than one code can be needed to describe the source diagnosis. Confirm with contextual judgment.
ICD-9-CM
517.2 Syst sclerosis lung dis
ApproximateCombination The match is approximate, and more than one code can be needed to describe the source diagnosis. Confirm with contextual judgment.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About M34.81Overview

Is M34.81 (Other forms of systemic sclerosis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report systemic sclerosis with lung involvement on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does M34.81 group to?

When systemic sclerosis with lung involvement is the principal diagnosis on an inpatient stay, it groups to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of M34.81?

Under the General Equivalence Mappings, systemic sclerosis with lung involvement converts to ICD-9-CM 710.1 (systemic sclerosis) and 517.2 (syst sclerosis lung dis). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.