ICD-10-CM Code I27.21

Secondary pulmonary arterial hypertension

Version 2021 Billable Code

Valid for Submission

I27.21 is a billable code used to specify a medical diagnosis of secondary pulmonary arterial hypertension. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code I27.21 might also be used to specify conditions or terms like associated pulmonary arterial hypertension, associated pulmonary arterial hypertension, pulmonary arterial hypertension associated with chronic hemolytic anemia, pulmonary arterial hypertension associated with congenital heart disease, pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt, pulmonary arterial hypertension associated with connective tissue disease, etc

ICD-10:I27.21
Short Description:Secondary pulmonary arterial hypertension
Long Description:Secondary pulmonary arterial hypertension

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code I27.21:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
  • (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

Code Also

Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • associated conditions if applicable, or adverse effects of drugs or toxins, such as:
  • adverse effect of appetite depressants T50.5X5
  • congenital heart disease Q20 Q28
  • human immunodeficiency virus HIV disease B20
  • polymyositis M33.2
  • portal hypertension K76.6
  • rheumatoid arthritis M05
  • schistosomiasis B65
  • Sjögren syndrome M35.0
  • systemic sclerosis M34

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code I27.21 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Associated pulmonary arterial hypertension
  • Associated pulmonary arterial hypertension
  • Pulmonary arterial hypertension associated with chronic hemolytic anemia
  • Pulmonary arterial hypertension associated with congenital heart disease
  • Pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt
  • Pulmonary arterial hypertension associated with connective tissue disease
  • Pulmonary arterial hypertension associated with HIV infection
  • Pulmonary arterial hypertension associated with schistosomiasis
  • Pulmonary arterial hypertension induced by drug
  • Pulmonary arterial hypertension induced by toxin
  • Secondary pulmonary hypertension
  • Small vessel pulmonary hypertension
  • Small vessel pulmonary hypertension
  • Solitary pulmonary hypertension
  • Solitary pulmonary hypertension

Diagnostic Related Groups

The ICD-10 code I27.21 is grouped in the following groups for version MS-DRG V38.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2020 through 09/30/2021.

  • 314 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC
  • 315 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC
  • 316 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC

Replacement Code

I2721 replaces the following previously assigned ICD-10 code(s):

  • I27.2 - Other secondary pulmonary hypertension

Convert I27.21 to ICD-9

  • 416.8 - Chr pulmon heart dis NEC (Approximate Flag)

Code Classification

  • Diseases of the circulatory system (I00–I99)
    • Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
      • Other pulmonary heart diseases (I27)

Code History

  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Pulmonary Hypertension

Also called: Pulmonary arterial hypertension

Pulmonary hypertension (PH) is high blood pressure in the arteries to your lungs. It is a serious condition. If you have it, the blood vessels that carry blood from your heart to your lungs become hard and narrow. Your heart has to work harder to pump the blood through. Over time, your heart weakens and cannot do its job and you can develop heart failure.

Symptoms of PH include

  • Shortness of breath during routine activity, such as climbing two flights of stairs
  • Tiredness
  • Chest pain
  • A racing heartbeat
  • Pain on the upper right side of the abdomen
  • Decreased appetite

As PH worsens, you may find it hard to do any physical activities.

There are two main kinds of PH. One runs in families or appears for no known reason. The other kind is related to another condition, usually heart or lung disease.

There is no cure for PH. Treatments can control symptoms. They involve treating the heart or lung disease, medicines, oxygen, and sometimes lung transplantation.

NIH: National Heart, Lung, and Blood Institute

  • Cor pulmonale (Medical Encyclopedia)
  • Lung diffusion testing (Medical Encyclopedia)
  • Pulmonary angiography (Medical Encyclopedia)
  • Pulmonary hypertension (Medical Encyclopedia)

[Learn More]

Pulmonary arterial hypertension Pulmonary arterial hypertension is a progressive disorder characterized by abnormally high blood pressure (hypertension) in the pulmonary artery, the blood vessel that carries blood from the heart to the lungs. Pulmonary arterial hypertension is one form of a broader condition known as pulmonary hypertension. Pulmonary hypertension occurs when most of the very small arteries throughout the lungs narrow in diameter, which increases the resistance to blood flow through the lungs. To overcome the increased resistance, blood pressure increases in the pulmonary artery and in the right ventricle of the heart, which is the chamber that pumps blood into the pulmonary artery. Ultimately, the increased blood pressure can damage the right ventricle of the heart.Signs and symptoms of pulmonary arterial hypertension occur when increased blood pressure cannot fully overcome the elevated resistance. As a result, the flow of oxygenated blood from the lungs to the rest of the body is insufficient. Shortness of breath (dyspnea) during exertion and fainting spells are the most common symptoms of pulmonary arterial hypertension. People with this disorder may experience additional symptoms, particularly as the condition worsens. Other symptoms include dizziness, swelling (edema) of the ankles or legs, chest pain, and a rapid heart rate.
[Learn More]