2026 ICD-10-CM Diagnosis Code J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere

ICD-10-CM CodesJ00–J99J80-J84J84

ICD-10-CM J84.170
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

J84.170 is a billable ICD-10-CM diagnosis code for interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. The code is a manifestation code that cannot be reported as the principal diagnosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified lower respiratory disease.

Code Identity

ICD-10-CM Code
J84.170
Billable Status
Yes — Valid for Submission
Code Describes
Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
Short Description
Interstit lung dis w progr fibrotic phenotype dis classd e
Parent Code
Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Code Classification

ChapterJ00–J99Diseases of the respiratory system
SectionJ80-J84Other respiratory diseases principally affecting the interstitium
CategoryJ84Other interstitial pulmonary diseases
This CodeJ84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere

Code EditsBilling

Medicare Code Editor checks that affect claim validity for J84.170.

Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and therefore should not be used as a principal diagnosis.

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Progressive fibrotic interstitial lung disease

Code First

  • underlying disease, such as:
  • lung diseases due to external agents J60 J70
  • rheumatoid arthritis M05.00 M06.9
  • sarcoidosis D86
  • systemic connective tissue disorders M30 M36

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • lung
        • interstitial
          • with progressive fibrotic phenotype, in diseases classified elsewhere

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR RSP016
Other specified and unspecified lower respiratory disease
Default principal diagnosis: inpatient No · outpatient No

Patient EducationClinical

Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement J84.170 replaces the following previously assigned code(s):

  • J84.17 - Oth interstit pulmon dis w fibrosis in dis classd elswhr
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About J84.170Overview

Is J84.170 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does J84.170 group to?

On inpatient claims, interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere maps to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.

Can J84.170 be a principal diagnosis?

No. This is a manifestation code: interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere describes the manifestation of an underlying disease rather than the disease itself, so the underlying condition is sequenced first.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.