2026 ICD-10-CM Diagnosis Code I27.841Fontan-associated lymphatic dysfunction
I27.841 is a billable ICD-10-CM diagnosis code for fontan-associated lymphatic dysfunction. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 808 through 810.
Code Identity
Code Classification
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Code Also
- associated conditions such as:
- chylothorax J94.0
- Fontan associated protein-losing enteropathy K90.89
- plastic obstructive bronchitis J44.89
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Fontan-associated - I27.841
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Circulation
- Fontan related
- with
- Fontan-associated lymphatic dysfunction
- Dysfunction
- lymphatic
- Fontan-associated
Code History & ChangesHistory
New Code I27.841 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.
Replacement I27.841 replaces the following previously assigned code(s):
- I27.89 - Other specified pulmonary heart diseases
Questions About I27.841Overview
Is I27.841 (Fontan related circulation) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report fontan-associated lymphatic dysfunction on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does I27.841 group to?
When fontan-associated lymphatic dysfunction is the principal diagnosis on an inpatient stay, it groups to MS-DRG 808, 809, 810, with relative weights from 1.0466 to 2.2079 depending on complications. Higher weights mean higher Medicare reimbursement.
