Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

ICD-10 codes I26-I28 classify conditions related to pulmonary heart disease and disorders of the pulmonary circulation, including pulmonary embolism, various forms of pulmonary hypertension, and diseases affecting pulmonary vessels. These codes specify conditions ranging from acute pulmonary embolism to chronic pulmonary hypertension and congenital or acquired pulmonary vessel abnormalities.

This range begins with I26, covering pulmonary embolism such as septic pulmonary embolism or saddle embolus, often specifying whether acute right heart strain (acute cor pulmonale) is present. The I27 codes describe other pulmonary heart diseases like primary pulmonary hypertension (also known as idiopathic or heritable pulmonary arterial hypertension), secondary pulmonary hypertension due to lung, heart or systemic causes, and chronic complications such as cor pulmonale. The range also includes Eisenmenger's syndrome and various other pulmonary hypertension types linked to conditions like lung disease or left heart disease. The final subset, I28, identifies other diseases of pulmonary vessels such as pulmonary artery aneurysms or arteriovenous fistulas. These detailed codes assist healthcare professionals and coders in accurately identifying pulmonary vascular and heart conditions for clinical, billing, and epidemiological purposes.

  • Diseases of the circulatory system (I00–I99)

    • Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

        • Pulmonary embolism (I26)

        • I26 Pulmonary embolism
        • I26.0 Pulmonary embolism with acute cor pulmonale
        • I26.01 Septic pulmonary embolism with acute cor pulmonale
        • I26.02 Saddle embolus of pulmonary artery with acute cor pulmonale
        • I26.03 Cement embolism of pulmonary artery with acute cor pulmonale
        • I26.04 Fat embolism of pulmonary artery with acute cor pulmonale
        • I26.09 Other pulmonary embolism with acute cor pulmonale
        • I26.9 Pulmonary embolism without acute cor pulmonale
        • I26.90 Septic pulmonary embolism without acute cor pulmonale
        • I26.92 Saddle embolus of pulmonary artery without acute cor pulmonale
        • I26.93 Single subsegmental thrombotic pulmonary embolism without acute cor pulmonale
        • I26.94 Multiple subsegmental thrombotic pulmonary emboli without acute cor pulmonale
        • I26.95 Cement embolism of pulmonary artery without acute cor pulmonale
        • I26.96 Fat embolism of pulmonary artery without acute cor pulmonale
        • I26.99 Other pulmonary embolism without acute cor pulmonale
        • Other pulmonary heart diseases (I27)

        • I27 Other pulmonary heart diseases
        • I27.0 Primary pulmonary hypertension
        • I27.1 Kyphoscoliotic heart disease
        • I27.2 Other secondary pulmonary hypertension
        • I27.20 Pulmonary hypertension, unspecified
        • I27.21 Secondary pulmonary arterial hypertension
        • I27.22 Pulmonary hypertension due to left heart disease
        • I27.23 Pulmonary hypertension due to lung diseases and hypoxia
        • I27.24 Chronic thromboembolic pulmonary hypertension
        • I27.29 Other secondary pulmonary hypertension
        • I27.8 Other specified pulmonary heart diseases
        • I27.81 Cor pulmonale (chronic)
        • I27.82 Chronic pulmonary embolism
        • I27.83 Eisenmenger's syndrome
        • I27.84 Fontan related circulation
        • I27.840 Fontan-associated liver disease [FALD] NEW CODE
        • I27.841 Fontan-associated lymphatic dysfunction NEW CODE
        • I27.848 Other Fontan-associated condition NEW CODE
        • I27.849 Fontan related circulation, unspecified NEW CODE
        • I27.89 Other specified pulmonary heart diseases
        • I27.9 Pulmonary heart disease, unspecified