Other pulmonary heart diseases (I27)
The ICD-10 code section I27 covers various other pulmonary heart diseases, which are heart conditions caused by or associated with lung or pulmonary vascular problems. These codes are specifically used to classify different types of pulmonary hypertension and other related heart diseases affecting the right side of the heart.
This section includes primary pulmonary hypertension (I27.0), also known by synonyms such as idiopathic pulmonary arterial hypertension and Ayerza's syndrome, referring to high blood pressure in lung arteries with no apparent cause. Codes like I27.21 specify secondary pulmonary arterial hypertension, which may result from connective tissue diseases, HIV, or congenital heart problems. Codes I27.22 and I27.23 describe pulmonary hypertension due to left heart disease or lung diseases and hypoxia, respectively. The code I27.24 identifies chronic thromboembolic pulmonary hypertension, a condition caused by blood clots in the lungs. Additionally, I27.81 covers cor pulmonale (chronic), a chronic right ventricular failure linked to pulmonary vascular disease. These codes help healthcare providers and coders accurately document the underlying causes and complications of pulmonary-related heart disease using the ICD-10 classification system.
Diseases of the circulatory system (I00–I99)
Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
I27 Other pulmonary heart diseases
- I27.0 Primary pulmonary hypertension
- I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
- I27.20 Pulmonary hypertension, unspecified
- I27.21 Secondary pulmonary arterial hypertension
- I27.22 Pulmonary hypertension due to left heart disease
- I27.23 Pulmonary hypertension due to lung diseases and hypoxia
- I27.24 Chronic thromboembolic pulmonary hypertension
- I27.29 Other secondary pulmonary hypertension
I27.8 Other specified pulmonary heart diseases
- I27.81 Cor pulmonale (chronic)
- I27.82 Chronic pulmonary embolism
- I27.83 Eisenmenger's syndrome
- I27.89 Other specified pulmonary heart diseases
- I27.9 Pulmonary heart disease, unspecified
Other pulmonary heart diseases (I27)
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Familial Primary Pulmonary Hypertension
Familial or idiopathic hypertension in the PULMONARY CIRCULATION which is not secondary to other disease.
Pulmonary Arterial Hypertension
A progressive rare pulmonary disease characterized by high blood pressure in the PULMONARY ARTERY.
Pulmonary Artery
The short wide vessel arising from the conus arteriosus of the right ventricle and conveying unaerated blood to the lungs.
Pulmonary Circulation
The circulation of the BLOOD through the LUNGS.
Pulmonary Heart Disease
Hypertrophy and dilation of the RIGHT VENTRICLE of the heart that is caused by PULMONARY HYPERTENSION. This condition is often associated with pulmonary parenchymal or vascular diseases, such as CHRONIC OBSTRUCTIVE PULMONARY DISEASE and PULMONARY EMBOLISM.
