Other pulmonary heart diseases (I27) ICD-10-CM
The I27 code range covers other pulmonary heart diseases with 21 ICD-10-CM diagnosis codes. 17 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the I27 Range 21 codes · 17 billable
- I27 Other pulmonary heart diseasesNon-billable
- I27.0 Primary pulmonary hypertension
- I27.1 Kyphoscoliotic heart disease
- I27.2 Other secondary pulmonary hypertensionNon-billable
- I27.20 Pulmonary hypertension, unspecified
- I27.21 Secondary pulmonary arterial hypertension
- I27.22 Pulmonary hypertension due to left heart disease
- I27.23 Pulmonary hypertension due to lung diseases and hypoxia
- I27.24 Chronic thromboembolic pulmonary hypertension
- I27.29 Other secondary pulmonary hypertension
- I27.8 Other specified pulmonary heart diseasesNon-billable
- I27.81 Cor pulmonale (chronic)
- I27.82 Chronic pulmonary embolism
- I27.83 Eisenmenger's syndrome
- I27.84 Fontan related circulationNon-billable
- I27.840 Fontan-associated liver disease [FALD]
- I27.841 Fontan-associated lymphatic dysfunction
- I27.848 Other Fontan-associated condition
- I27.849 Fontan related circulation, unspecified
- I27.89 Other specified pulmonary heart diseases
- I27.9 Pulmonary heart disease, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the I27 range.
Chronic Pulmonary Embolism
Persistent and long-standing pulmonary embolism.
Chronic Thromboembolic Pulmonary Hypertension
Persistent and long-standing pulmonary hypertension caused by recurrent blood clots in the pulmonary arteries.
Eisenmenger Complex
A condition associated with VENTRICULAR SEPTAL DEFECT and other congenital heart defects that allow the mixing of pulmonary and systemic circulation, increase blood flow into the lung, and subsequent responses to low oxygen in blood. This complex is characterized by progressive PULMONARY HYPERTENSION; HYPERTROPHY of the RIGHT VENTRICLE; CYANOSIS; and ERYTHROCYTOSIS.
Hypertension, Pulmonary
Increased VASCULAR RESISTANCE in the PULMONARY CIRCULATION, usually secondary to HEART DISEASES or LUNG DISEASES.
Primary Pulmonary Hypertension
Pulmonary hypertension that is not caused by any other disease or condition.
Pulmonary Heart Disease
Hypertrophy and dilation of the RIGHT VENTRICLE of the heart that is caused by PULMONARY HYPERTENSION. This condition is often associated with pulmonary parenchymal or vascular diseases, such as CHRONIC OBSTRUCTIVE PULMONARY DISEASE and PULMONARY EMBOLISM.
About the I27 Code Range
These conditions involve the heart or blood circulation in the lungs. They include pulmonary hypertension, or high blood pressure in the lungs.
The main branches distinguish primary pulmonary hypertension (I27.0), kyphoscoliotic heart disease (I27.1), and other secondary pulmonary hypertension (I27.2). Other specified pulmonary heart diseases (I27.8) and unspecified pulmonary heart disease (I27.9) form the remaining branches.
The secondary pulmonary hypertension branch separates an unspecified form from forms linked to the lung arteries, left heart disease, lung disease and low oxygen, or chronic blood clots. The other specified branch separates named conditions and Fontan related circulation. Fontan related circulation divides further by associated liver disease, lymphatic dysfunction, other conditions, or an unspecified form.
Questions About This Page
How many billable codes are in the I27 range?
Of the 21 codes in this range, 17 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the I27 range classify?
The range classifies other pulmonary heart diseases. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
