Other pulmonary heart diseases (I27) ICD-10-CM
The I27 code range covers other pulmonary heart diseases with 21 ICD-10-CM diagnosis codes. 17 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the I27 Range 21 codes · 17 billable
- I27 Other pulmonary heart diseasesNon-billable
- I27.0 Primary pulmonary hypertension
- I27.1 Kyphoscoliotic heart disease
- I27.2 Other secondary pulmonary hypertensionNon-billable
- I27.20 Pulmonary hypertension, unspecified
- I27.21 Secondary pulmonary arterial hypertension
- I27.22 Pulmonary hypertension due to left heart disease
- I27.23 Pulmonary hypertension due to lung diseases and hypoxia
- I27.24 Chronic thromboembolic pulmonary hypertension
- I27.29 Other secondary pulmonary hypertension
- I27.8 Other specified pulmonary heart diseasesNon-billable
- I27.81 Cor pulmonale (chronic)
- I27.82 Chronic pulmonary embolism
- I27.83 Eisenmenger's syndrome
- I27.84 Fontan related circulationNon-billable
- I27.840 Fontan-associated liver disease [FALD] New
- I27.841 Fontan-associated lymphatic dysfunction New
- I27.848 Other Fontan-associated condition New
- I27.849 Fontan related circulation, unspecified New
- I27.89 Other specified pulmonary heart diseases
- I27.9 Pulmonary heart disease, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the I27 range.
Familial Primary Pulmonary Hypertension
Familial or idiopathic hypertension in the PULMONARY CIRCULATION which is not secondary to other disease.
Pulmonary Arterial Hypertension
A progressive rare pulmonary disease characterized by high blood pressure in the PULMONARY ARTERY.
Pulmonary Artery
The short wide vessel arising from the conus arteriosus of the right ventricle and conveying unaerated blood to the lungs.
Pulmonary Circulation
The circulation of the BLOOD through the LUNGS.
Pulmonary Heart Disease
Hypertrophy and dilation of the RIGHT VENTRICLE of the heart that is caused by PULMONARY HYPERTENSION. This condition is often associated with pulmonary parenchymal or vascular diseases, such as CHRONIC OBSTRUCTIVE PULMONARY DISEASE and PULMONARY EMBOLISM.
About the I27 Code Range
The ICD-10 code section I27 covers various other pulmonary heart diseases, which are heart conditions caused by or associated with lung or pulmonary vascular problems. These codes are specifically used to classify different types of pulmonary hypertension and other related heart diseases affecting the right side of the heart.
This section includes primary pulmonary hypertension (I27.0), also known by synonyms such as idiopathic pulmonary arterial hypertension and Ayerza's syndrome, referring to high blood pressure in lung arteries with no apparent cause. Codes like I27.21 specify secondary pulmonary arterial hypertension, which may result from connective tissue diseases, HIV, or congenital heart problems. Codes I27.22 and I27.23 describe pulmonary hypertension due to left heart disease or lung diseases and hypoxia, respectively. The code I27.24 identifies chronic thromboembolic pulmonary hypertension, a condition caused by blood clots in the lungs. Additionally, I27.81 covers cor pulmonale (chronic), a chronic right ventricular failure linked to pulmonary vascular disease. These codes help healthcare providers and coders accurately document the underlying causes and complications of pulmonary-related heart disease using the ICD-10 classification system.
Questions About This Page
How many billable codes are in the I27 range?
Of the 21 codes in this range, 17 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the I27 range classify?
The range classifies other pulmonary heart diseases. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
