Other diseases of pulmonary vessels (I28) ICD-10-CM
The I28 code range covers other diseases of pulmonary vessels with 5 ICD-10-CM diagnosis codes. 4 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the I28 Range 5 codes · 4 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the I28 range.
Endarteritis
Inflammation of the inner endothelial lining (TUNICA INTIMA) of an artery.
Tunica Intima
The innermost layer of an artery or vein, made up of one layer of endothelial cells and supported by an internal elastic lamina.
About the I28 Code Range
ICD-10 code section I28 is designated for other diseases of pulmonary vessels, addressing conditions affecting the blood vessels within the lungs beyond common classifications. These codes capture a range of rare or complex pulmonary vascular disorders.
This section includes I28.0 for arteriovenous fistula of pulmonary vessels, which covers abnormal connections such as pulmonary arteriovenous malformations or aneurysms, sometimes seen after surgeries like superior cavopulmonary anastomosis and related to conditions like TEMPI syndrome. The code I28.1 applies to aneurysms of the pulmonary artery, including rupture, dilatation, or injury to these vessels, a critical concern due to risk of blood flow disruption and vessel damage. I28.8 is a broad category capturing various other pulmonary vessel diseases such as postoperative stenosis, pulmonary arteritis, and multiple stenoses or obstructions of pulmonary veins or arteries, often resulting from congenital or acquired causes including surgery-related complications. Lastly, I28.9 denotes unspecified diseases of pulmonary vessels, used when a pulmonary vascular condition is diagnosed but not further defined. Medical coders use these codes to identify and document specific pulmonary vascular abnormalities that impact pulmonary circulation and heart function accurately.
Questions About This Page
How many billable codes are in the I28 range?
Of the 5 codes in this range, 4 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the I28 range classify?
The range classifies other diseases of pulmonary vessels. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
