Other diseases of pulmonary vessels (I28)

ICD-10 code section I28 is designated for other diseases of pulmonary vessels, addressing conditions affecting the blood vessels within the lungs beyond common classifications. These codes capture a range of rare or complex pulmonary vascular disorders.

This section includes I28.0 for arteriovenous fistula of pulmonary vessels, which covers abnormal connections such as pulmonary arteriovenous malformations or aneurysms, sometimes seen after surgeries like superior cavopulmonary anastomosis and related to conditions like TEMPI syndrome. The code I28.1 applies to aneurysms of the pulmonary artery, including rupture, dilatation, or injury to these vessels, a critical concern due to risk of blood flow disruption and vessel damage. I28.8 is a broad category capturing various other pulmonary vessel diseases such as postoperative stenosis, pulmonary arteritis, and multiple stenoses or obstructions of pulmonary veins or arteries, often resulting from congenital or acquired causes including surgery-related complications. Lastly, I28.9 denotes unspecified diseases of pulmonary vessels, used when a pulmonary vascular condition is diagnosed but not further defined. Medical coders use these codes to identify and document specific pulmonary vascular abnormalities that impact pulmonary circulation and heart function accurately.