Acute rheumatic fever (I00-I02) ICD-10-CM
The I00–I02 section covers acute rheumatic fever with 10 ICD-10-CM diagnosis codes, of which 8 are billable in fiscal year 2026. The section is organized into the 3 code ranges listed below.
Code Ranges in This Section 3 ranges · 10 codes
| Code Range | Title | Codes | Billable |
|---|---|---|---|
| I00 | Rheumatic fever without heart involvement (I00) | 1 | 1 |
| I01 | Rheumatic fever with heart involvement (I01) | 6 | 5 |
| I02 | Rheumatic chorea (I02) | 3 | 2 |
The info icon previews the code ranges inside each row and its instructional notations from the official Tabular List.
About the I00–I02 Code Range
ICD-10 codes I00-I02 specifically categorize acute rheumatic fever, distinguishing cases based on whether the heart is affected. These codes cover a spectrum from rheumatic fever without heart involvement to various forms of acute rheumatic heart disease and rheumatic chorea.
This range begins with I00, used for acute rheumatic fever without heart involvement, also known as migratory polyarthritis or erythema marginatum. Codes from I01 address acute rheumatic fever when the heart is involved, including conditions like acute rheumatic pericarditis (I01.0), endocarditis (I01.1), and myocarditis (I01.2). These specify inflammation of different heart layers during rheumatic fever. Code I01.8 captures other specified acute rheumatic heart diseases, and I01.9 is used when the heart condition is unspecified. Additionally, I02 covers rheumatic chorea, a neurological disorder linked with rheumatic fever, with subcodes differentiating cases with or without heart involvement. Recognizing terms such as rheumatic arthritis or autoimmune movement disorder helps coders assign these codes accurately for both cardiac and neurological sequelae following a streptococcal infection.
Questions About This Page
How many codes are in the I00-I02 range?
The I00-I02 range contains 10 ICD-10-CM diagnosis codes in FY 2026. 8 of them are billable, and the rest are category headers that organize the section.
What conditions does I00-I02 cover?
The range covers acute rheumatic fever. The code ranges listed above break it into groups of related conditions, and each one links to its own page with the full code list.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
