2027 ICD-10-CM Diagnosis Code G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
ICD-10-CM Codes›G00–G99›G70-G73›G71
- Billable — Valid for Submission
- Risk Adjusts — HCC 197
- 7th Character 2
- Chronic Condition
G71.0342 is a billable ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 91 through 93. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.
For Medicare Advantage risk adjustment, G71.0342 maps to CMS-HCC Category 197 (Muscular Dystrophy) under the V28 model, adding a risk factor of about 0.426 for a community, non-dual, aged beneficiary in payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
G71.0342 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to G71.0342: its own notes plus those printed at G71 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Beta sarcoglycanopathy
- Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
- Limb girdle muscular dystrophy type 2E
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name G71.0342, its category, or a range that includes it.
Excludes2 1
These codes carry an Excludes2 note naming G71.0342: its condition is not part of those codes, and both may be reported when the patient has both.
- Block M60-M63 Disorders of muscles
Code First 2
These codes say to code first a condition named in the note, and G71.0342 is one of the conditions named.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
beta sarcoglycan dysfunction G71.0342
R4 (autosomal recessive) G71.0342
type 2E (autosomal recessive) G71.0342
beta G71.0342
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Muscular Dystrophies, Limb-Girdle
a heterogenous group of inherited muscular dystrophy that can be autosomal dominant or autosomal recessive. there are many forms (called lgmds) involving genes encoding muscle membrane proteins such as the sarcoglycan (sarcoglycans) complex that interacts with dystrophin. the disease is characterized by progressing wasting and weakness of the proximal muscles of arms and legs around the hips and shoulders (the pelvic and shoulder girdles).
Code History & ChangesHistory
Replacement G71.0342 replaces the following previously assigned code(s):
- G71.09 - Other specified muscular dystrophies
Questions About G71.0342Overview
What is the ICD-10 code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction?
The ICD-10-CM code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction is G71.0342 (sometimes written as G710342). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is G71.0342 a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report limb girdle muscular dystrophy due to beta sarcoglycan dysfunction on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does G71.0342 group to?
When limb girdle muscular dystrophy due to beta sarcoglycan dysfunction is the principal diagnosis on an inpatient stay, it groups to MS-DRG 91, 92, 93, with relative weights from 0.7783 to 1.7050 depending on complications. Higher weights mean higher Medicare reimbursement.
What HCC is G71.0342?
G71.0342 (limb girdle muscular dystrophy due to beta sarcoglycan dysfunction) maps to CMS-HCC Category 197 (Muscular Dystrophy), commonly written as HCC 197, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 76 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.
Does G71.0342 risk-adjust for Medicare Advantage payment?
Yes. When documented and reported on a Medicare Advantage encounter, G71.0342 adds a risk adjustment factor of about 0.426 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.145 to 0.681 depending on the payment segment). HCC 197 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 197 category page.
