2026 ICD-10-CM Diagnosis Code G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.0342
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.0342 is a billable ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.0342
Billable Status
Yes — Valid for Submission
Code Describes
Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
Short Description
Limb girdle musc dyst due to beta sarcoglycan dysfunction
Parent Code
G71.034
Limb girdle muscular dystrophy due to sarcoglycan dysfunction

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Beta sarcoglycanopathy
  • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2E

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • beta-sarcoglycan-related
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • due to
            • beta sarcoglycan dysfunction
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R4 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2E (autosomal recessive)
    • Sarcoglycanopathy
      • beta

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement G71.0342 replaces the following previously assigned code(s):

  • G71.09 - Other specified muscular dystrophies
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.0342Overview

Is G71.0342 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report limb girdle muscular dystrophy due to beta sarcoglycan dysfunction on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.