2026 ICD-10-CM Diagnosis Code G71.031Autosomal dominant limb girdle muscular dystrophy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.031
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.031 is a billable ICD-10-CM diagnosis code for autosomal dominant limb girdle muscular dystrophy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as autosomal dominant limb girdle muscular dystrophy type 1D. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.031
Billable Status
Yes — Valid for Submission
Code Describes
Autosomal dominant limb girdle muscular dystrophy
Short Description
Autosomal dominant limb girdle muscular dystrophy
Same as the full description in the CMS dataset.
Parent Code
G71.03
Limb girdle muscular dystrophies

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.031Autosomal dominant limb girdle muscular dystrophy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant limb girdle muscular dystrophy type 1D
  • Autosomal dominant limb girdle muscular dystrophy type 1E
  • Autosomal dominant limb girdle muscular dystrophy type 1F
  • Autosomal dominant limb girdle muscular dystrophy type 1G
  • Autosomal dominant limb-girdle muscular dystrophy type 1H
  • Autosomal dominant muscular dystrophy with limb girdle distribution
  • Calpain-3-related limb girdle muscular dystrophy D4

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • LGMD D4 calpain-3-related
  • LGMD D5 collagen 6-related
  • Limb girdle muscular dystrophy type 1

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Calpainopathy(primary)
      • autosomal dominant
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • calpain-3-related
            • autosomal dominant
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • collagen VI related
            • autosomal dominant
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • D1 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • D2 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • D3 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • D4 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • D5 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1 (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1A (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1B (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1C (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1E (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1H (autosomal dominant)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 1I (autosomal dominant)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement G71.031 replaces the following previously assigned code(s):

  • G71.09 - Other specified muscular dystrophies
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.031Overview

Is G71.031 (Limb girdle muscular dystrophies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report autosomal dominant limb girdle muscular dystrophy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.