2027 ICD-10-CM Diagnosis Code G71.031Autosomal dominant limb girdle muscular dystrophy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.031
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G71.031 is a billable ICD-10-CM diagnosis code for autosomal dominant limb girdle muscular dystrophy. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 91 through 93. Coders also document this condition as autosomal dominant limb girdle muscular dystrophy type 1D. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

For Medicare Advantage risk adjustment, G71.031 maps to CMS-HCC Category 197 (Muscular Dystrophy) under the V28 model, adding a risk factor of about 0.426 for a community, non-dual, aged beneficiary in payment year 2027.

Code Identity

ICD-10-CM Code
G71.031
Billable Status
Yes — Valid for Submission
Code Describes
Autosomal dominant limb girdle muscular dystrophy
Short Description
Autosomal dominant limb girdle muscular dystrophy
Same as the full description in the CMS dataset.
Parent Code
G71.03
Limb girdle muscular dystrophies

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.031Autosomal dominant limb girdle muscular dystrophy

Medicare Risk Adjustment (HCC)Billing

G71.031 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.

CMS-HCC V28 Category (Payment Model)
HCC 197— Muscular Dystrophy
Payment HCC · PY 2027 one of 21 ICD-10-CM codes in this category
Risk Adjustment Factor (RAF) Weight
+0.426
community, non-dual, aged · ranges 0.145–0.681 across segments
Hierarchy
Top of its hierarchy
HCC 197 is not superseded by any other condition category
Prior Model (CMS-HCC V24)
HCC 76
V24 retired V28 pays 100% of MA risk scores since PY 2026
Other CMS Models
PACE (CMS-HCC V22): HCC 76 · ESRD (V21): HCC 76 · ESRD (V24): HCC 76
ESRD V21 weights: 0.062 dialysis, 0.296–0.544 functioning graft · ESRD V24 weights: 0.136 dialysis, 0.322–0.842 functioning graft
Part D (RxHCC)
Not mapped
G71.031 does not risk-adjust in the RxHCC prescription drug model

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant limb girdle muscular dystrophy type 1D
  • Autosomal dominant limb girdle muscular dystrophy type 1E
  • Autosomal dominant limb girdle muscular dystrophy type 1F
  • Autosomal dominant limb girdle muscular dystrophy type 1G
  • Autosomal dominant limb-girdle muscular dystrophy type 1H
  • Autosomal dominant muscular dystrophy with limb girdle distribution
  • Calpain-3-related limb girdle muscular dystrophy D4

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G71.031: its own notes plus those printed at G71 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • LGMD D4 calpain-3-related
  • LGMD D5 collagen 6-related
  • Limb girdle muscular dystrophy type 1

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From G71 Primary disorders of muscles applies to 28 codes
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name G71.031, its category, or a range that includes it.

Excludes2 1

These codes carry an Excludes2 note naming G71.031: its condition is not part of those codes, and both may be reported when the patient has both.

  • Block M60-M63 Disorders of muscles
    muscular dystrophies and myopathies (G71-G72) names G71-G72, which includes this code

Code First 2

These codes say to code first a condition named in the note, and G71.031 is one of the conditions named.

  • M62.84 Sarcopenia
    primary disorders of muscles (G71.-) names G71.-, which includes this code
  • Z99.3 Dependence on wheelchair
    muscular dystrophy (G71.0-) names G71.0-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Muscular Dystrophies, Limb-Girdle

    a heterogenous group of inherited muscular dystrophy that can be autosomal dominant or autosomal recessive. there are many forms (called lgmds) involving genes encoding muscle membrane proteins such as the sarcoglycan (sarcoglycans) complex that interacts with dystrophin. the disease is characterized by progressing wasting and weakness of the proximal muscles of arms and legs around the hips and shoulders (the pelvic and shoulder girdles).

Code History & ChangesHistory

Replacement G71.031 replaces the following previously assigned code(s):

  • G71.09 - Other specified muscular dystrophies
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G71.031Overview

What is the ICD-10 code for autosomal dominant limb girdle muscular dystrophy?

The ICD-10-CM code for autosomal dominant limb girdle muscular dystrophy is G71.031 (sometimes written as G71031). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is G71.031 (Limb girdle muscular dystrophies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report autosomal dominant limb girdle muscular dystrophy on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does G71.031 group to?

When autosomal dominant limb girdle muscular dystrophy is the principal diagnosis on an inpatient stay, it groups to MS-DRG 91, 92, 93, with relative weights from 0.7783 to 1.7050 depending on complications. Higher weights mean higher Medicare reimbursement.

What HCC is G71.031?

G71.031 (autosomal dominant limb girdle muscular dystrophy) maps to CMS-HCC Category 197 (Muscular Dystrophy), commonly written as HCC 197, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 76 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.

Does G71.031 risk-adjust for Medicare Advantage payment?

Yes. When documented and reported on a Medicare Advantage encounter, G71.031 adds a risk adjustment factor of about 0.426 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.145 to 0.681 depending on the payment segment). HCC 197 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 197 category page.