2027 ICD-10-CM Diagnosis Code G31.89Other specified degenerative diseases of nervous system

Alternate terms and clinical phrases that map to this code.

• 3-Methylglutaconic aciduria type 4
• Acquired cerebellar atrophy
• Acute cerebellar syndrome
• Argyrophilic grain disease
• Arteriopathic granular atrophy of cerebral cortex
• Atrophy of cerebellar vermis
• Atrophy of corticospinal tract
• Atrophy of pyramidal tract
• Autoimmune cerebellar degeneration
• Autosomal dominant striatal neurodegeneration
• Autosomal recessive cerebral atrophy
• Beta-propeller protein-associated neurodegeneration
• Cerebellar ataxia associated with another disorder
• Cerebellar deficiency syndrome
• Cerebral degeneration in childhood
• Childhood-onset motor and cognitive regression syndrome with extrapyramidal movement disorder
• Chorea co-occurrent and due to dentatorubropallidoluysian degeneration
• Chorea co-occurrent and due to Huntington disease-like condition
• Chorea due to chronic hepatocerebral degeneration
• Chorea due to hereditary ataxia
• Chorea due to heredodegenerative disorder
• Chorea due to Huntington disease-like 1
• Chorea due to Huntington disease-like 2
• Chorea due to Huntington disease-like 3
• Choreoathetosis
• Chronic axonal neuropathy
• Chronic hepatocerebral degeneration
• CLCN6-related childhood-onset progressive neurodegeneration, peripheral neuropathy syndrome
• Coenzyme A synthase protein associated neurodegeneration
• Congenital cerebellar cortical atrophy
• Congenital microcephaly, severe encephalopathy, progressive cerebral atrophy syndrome
• Corneal cerebellar syndrome
• Cortical visual impairment
• Corticostriatal-spinal degeneration
• Cystic degeneration of brain
• Dentatorubropallidoluysian degeneration
• Diffuse atrophy of cerebellum
• Diffuse atrophy of cerebrum
• Diffuse cerebral and cerebellar atrophy, intractable seizures, progressive microcephaly syndrome
• Disorder of valine metabolism
• Early-onset neurodegeneration, choreoathetoid movement, microcytic anemia due to IREB2 mutation
• Early-onset progressive diffuse brain atrophy, microcephaly, muscle weakness, optic atrophy syndrome
• Early-onset progressive encephalopathy, hearing loss, pons hypoplasia, brain atrophy syndrome
• Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
• Fatal post-viral neurodegenerative disorder
• Fatty acid hydroxylase associated neurodegeneration
• Generalized dystonia
• Global brain atrophy
• Global developmental delay, visual anomalies, progressive cerebellar atrophy, truncal hypotonia syndrome
• Hereditary acantholytic dermatosis
• Hereditary degenerative disease of central nervous system
• Huntington disease-like 1
• Huntington disease-like 3
• Huntington disease-like syndrome
• Huntington disease-like syndrome due to C9ORF72 expansions
• Hypomyelinating leukodystrophy with atrophy of basal ganglia and cerebellum
• Inborn error of amino acid metabolism
• Infantile cerebral and cerebellar atrophy with postnatal progressive microcephaly
• Infantile neuroaxonal dystrophy
• Infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome
• Infantile spasms, psychomotor retardation, progressive brain atrophy, basal ganglia disease syndrome
• Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome
• Juvenile cerebellar degeneration AND myoclonus
• Keratosis follicularis, dwarfism, cerebral atrophy syndrome
• Kufor Rakeb syndrome
• Late cortical cerebellar atrophy
• Late infantile and juvenile neuroaxonal dystrophy
• MEGDEL syndrome
• MEPAN syndrome
• Mitochondrial membrane protein associated neurodegeneration
• NADHX dehydratase deficiency
• NADHX epimerase deficiency
• NESCAV syndrome
• Neuroaxonal dystrophy
• Neurodegeneration due to 3-hydroxyisobutyryl coenzyme A hydrolase deficiency
• Neurodevelopmental delay, seizures, ophthalmic anomalies, osteopenia, cerebellar atrophy syndrome
• Olivopontocerebellar atrophy and deafness
• Olivopontocerebellar degeneration
• PCNA-related progressive neurodegenerative photosensitivity syndrome
• Peripheral axonal neuropathy
• Pineal degeneration
• PRKAR1B-related neurodegenerative dementia with intermediate filaments
• Progressive cerebello-cerebral atrophy
• Progressive chorea
• Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
• Progressive neuronal degeneration of childhood
• Progressive neuronal degeneration without liver cirrhosis
• Progressive visual impairment
• Second cranial nerve finding
• Severe neurodegenerative syndrome with lipodystrophy
• Sporadic cerebellar degeneration
• Synucleinopathy
• TUBB4A-related leukodystrophy
• Type 1 diabetes mellitus, central and peripheral neurodegeneration syndrome
• USP18 deficiency
• X-linked neurodegenerative syndrome Bertini type
• X-linked neurodegenerative syndrome Hamel type

Instructions from the official ICD-10-CM Tabular List that apply to G31.89: its own notes plus those printed at G31 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Instructional notes printed at other codes that name G31.89, its category, or a range that includes it.

Alphabetical index entries that point to this code.

• Degeneration, degenerative

  • brain (cortical) (progressive) G31.9

    • childhood G31.9

      • specified NEC G31.89

    • cystic G31.89

  • cortical (cerebellar) (parenchymatous) G31.89

  • nervous system G31.9

    • fatty G31.89

    • specified NEC G31.89

  • spinal (cord) G31.89

    • familial NEC G31.89

    • fatty G31.89

• Dystrophy, dystrophia

  • infantile neuraxonal G31.89

• Seitelberger's syndrome (infantile neuraxonal dystrophy) G31.89

• Syndrome See Also: Disease;

  • Seitelberger's G31.89