2026 ICD-10-CM Diagnosis Code D61.02Shwachman-Diamond syndrome

ICD-10-CM Codes›D50–D89›D60-D64›D61

ICD-10-CM D61.02
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D61.02 is a billable ICD-10-CM diagnosis code for Shwachman-Diamond syndrome. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 808 through 810. Coders also document this condition as pancreatic insufficiency. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Aplastic anemia.

Code Identity

ICD-10-CM Code
D61.02
Billable Status
Yes — Valid for Submission
Code Describes
Shwachman-Diamond syndrome
Short Description
Shwachman-Diamond syndrome
Same as the full description in the CMS dataset.
Parent Code
D61.0
Constitutional aplastic anemia

Code Classification

ChapterD50–D89Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
SectionD60-D64Aplastic and other anemias and other bone marrow failure syndromes
CategoryD61Other aplastic anemias and other bone marrow failure syndromes
This CodeD61.02Shwachman-Diamond syndrome

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Pancreatic insufficiency
  • Shwachman syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Code Also

  • , if applicable, associated conditions such as:
  • acute myeloblastic leukemia C92.0
  • exocrine pancreatic insufficiency K86.81
  • myelodysplastic syndrome D46

Use Additional Code

  • code, if applicable, for genetic susceptibility to other malignant neoplasm Z15.09

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • Schwachman (-Diamond)
    • Syndrome
      • Shwachman (-Diamond)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR BLD003
Aplastic anemia
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement D61.02 replaces the following previously assigned code(s):

  • D61.09 - Other constitutional aplastic anemia
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D61.02Overview

Is D61.02 (Constitutional aplastic anemia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report Shwachman-Diamond syndrome on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does D61.02 group to?

When Shwachman-Diamond syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 808, 809, 810, with relative weights from 1.0466 to 2.2079 depending on complications. Higher weights mean higher Medicare reimbursement.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.