2026 ICD-10-CM Diagnosis Code Q89.09Congenital malformations of spleen

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.09
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.09 is a billable ICD-10-CM diagnosis code for congenital malformations of spleen. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 814 through 816. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.09
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformations of spleen
Short Description
Congenital malformations of spleen
Same as the full description in the CMS dataset.
Parent Code
Q89.0
Congenital absence and malformations of spleen

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.09Congenital malformations of spleen

Present on Admission (POA)Billing

Q89.09 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Accessory spleen
  • Bilateral left-sidedness sequence
  • Biliary atresia with splenic malformation syndrome
  • Congenital abnormal shape of spleen
  • Congenital anomaly of spleen
  • Congenital biliary atresia
  • Congenital cyst of spleen
  • Congenital hypoplasia of spleen
  • Congenital lobulation of spleen
  • Congenital malposition of spleen
  • Congenital splenomegaly
  • Ectopic spleen
  • Ectopic splenic tissue
  • Hereditary splenic hypoplasia
  • Hypoplasia of spleen
  • Laterality sequence
  • Mis-shapen spleen
  • Polycystic spleen
  • Polysplenia heterotaxy syndrome
  • Situs ambiguus
  • Spleen in right sided position
  • Splenic cyst
  • Splenogonadal fusion
  • Splenogonadal fusion, limb defect, micrognathia syndrome
  • Splenosis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital splenomegaly

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • spleen
    • Accessory(congenital)
      • spleen
    • Anomaly, anomalous(congenital) (unspecified type)
      • spleen
    • Cyst(colloid) (mucous) (simple) (retention)
      • spleen NEC
        • congenital
    • Deformity
      • spleen
        • congenital
    • Disease, diseased
      • polycystic
        • spleen
    • Disease, diseased
      • spleen
        • polycystic
    • Displacement, displaced
      • spleen (congenital)
    • Distortion(s) (congenital)
      • spleen
    • Ectopic, ectopia(congenital)
      • spleen
    • Lobulation(congenital)
      • spleen
    • Malformation(congenital)
      • spleen
    • Malposition
      • congenital
        • spleen
    • Polycystic(disease)
      • spleen
    • Polysplenia syndrome
    • Splenomegaly, splenomegalia(Bengal) (cryptogenic) (idiopathic) (tropical)
      • congenital
    • Supernumerary(congenital)
      • spleen
    • Syndrome
      • polysplenia

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Splenosis

    the spontaneous transplantation of splenic tissue to unusual sites after open splenic trauma, e.g., after automobile accidents, gunshot or stab wounds. the splenic pulp implants appear as red-blue nodules on the peritoneum, omentum, and mesentery, morphologically similar to multifocal pelvic endometriosis. (segen, dictionary of modern medicine, 1992)

  • Splenosis

    the presence of benign ectopic splenic tissue in the peritoneum.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
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  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.09 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.0 Anomalies of spleen
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.09Overview

Is Q89.09 (Congenital absence and malformations of spleen) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformations of spleen on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.09 group to?

When congenital malformations of spleen is the principal diagnosis on an inpatient stay, it groups to MS-DRG 814, 815, 816, with relative weights from 0.6320 to 2.1267 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.09 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformations of spleen on inpatient claims.

What is the ICD-9 equivalent of Q89.09?

Under the General Equivalence Mappings, congenital malformations of spleen converts to ICD-9-CM 759.0 (anomalies of spleen). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.