2026 ICD-10-CM Diagnosis Code Q87.88CTNNB1 syndrome
Q87.88 is a billable ICD-10-CM diagnosis code for CTNNB1 syndrome. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is exempt from POA reporting.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q87.88 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Use Additional Code
- code, if applicable, for associated conditions such as:
- cerebral palsy G80
- congenital heart malformations Q20.0 Q24.9
- developmental disorder of speech and language F80
- exudative retinopathy H35.02
- intellectual disability F70 F79
- microcephaly Q02
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
Index to Diseases and InjuriesGuidance
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Syndrome
- CTNNB1
Code History & ChangesHistory
New Code Q87.88 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.
Replacement Q87.88 replaces the following previously assigned code(s):
- Q87.89 - Oth congenital malformation syndromes, NEC
Questions About Q87.88Overview
Is Q87.88 a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report CTNNB1 syndrome on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
Is Q87.88 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for CTNNB1 syndrome on inpatient claims.
