2027 ICD-10-CM Diagnosis Code Q74.3Arthrogryposis multiplex congenita

ICD-10-CM Codes›Q00-Q99›Q65-Q79›s

ICD-10-CM Q74.3
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q74.3 is a billable ICD-10-CM diagnosis code for arthrogryposis multiplex congenita. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 5 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q74.3
Billable Status
Yes — Valid for Submission
Code Describes
Arthrogryposis multiplex congenita
Short Description
Arthrogryposis multiplex congenita
Same as the full description in the CMS dataset.
Parent Code
Q74
Other congenital malformations of limb(s)

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategorysOther congenital malformations of limb (Q74)
This CodeQ74.3Arthrogryposis multiplex congenita

Present on Admission (POA)Billing

Q74.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adducted thumbs and arthrogryposis syndrome Christian type
  • Akinesia
  • Antenatal multi-minicore disease with arthrogryposis multiplex congenita
  • Anterior horn cell disease
  • Arthrogryposis
  • Arthrogryposis and ectodermal dysplasia syndrome
  • Arthrogryposis hyperkeratosis syndrome lethal form
  • Arthrogryposis multiplex congenita
  • Arthrogryposis with oculomotor limitation and electroretinal anomaly
  • Arthrogryposis with renal dysfunction and cholestasis syndrome
  • Autism spectrum disorder, epilepsy, arthrogryposis syndrome
  • Autosomal recessive myogenic arthrogryposis multiplex congenita
  • Congenital arthrogryposis caused by teratogen
  • Congenital flexion contracture of foot joint
  • Congenital hypoplasia of breast
  • Congenital muscular dystrophy with arthrogryposis multiplex congenita
  • Digitotalar dysmorphism
  • Distal arthrogryposis syndrome
  • Distal arthrogryposis type 10
  • Distal arthrogryposis type 3
  • Distal arthrogryposis type 4
  • Distal arthrogryposis type 5D
  • Distal arthrogryposis type 6
  • Familial arthrogryposis-cholestatic hepatorenal syndrome
  • Hepatorenal syndrome
  • Hyperpyrexia
  • Hypomyelination neuropathy arthrogryposis syndrome
  • Hypoplasia of nipple
  • Illum syndrome
  • Inherited arthrogryposis
  • Inherited disorder of bilirubin metabolism
  • Joint contracture, webbed neck, micrognathia, hypoplastic nipple syndrome
  • Kuskokwim syndrome
  • Lethal arthrogryposis with anterior horn cell disease
  • Lethal congenital contracture syndrome type 1
  • Lethal congenital contracture syndrome type 2
  • Lethal congenital contracture syndrome type 3
  • Lethal congenital contracture syndrome type 5
  • Malignant hyperthermia
  • Malignant hyperthermia with arthrogryposis and torticollis syndrome
  • Morse Rawnsley Sargent syndrome
  • Multi-core congenital myopathy
  • MYBPC1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome
  • Neck webbing
  • Neurogenic arthrogryposis multiplex congenita
  • Pelvic dysplasia, arthrogryposis of lower limbs syndrome
  • Rozin Hertz Goodman syndrome
  • Sheldon-Hall syndrome
  • X-linked distal arthrogryposis multiplex congenita
  • X-linked distal hereditary motor neuropathy

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q74.3: its own notes plus those printed at Q74 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q74 Other congenital malformations of limb(s) applies to 6 codes

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q74.3, its category, or a range that includes it.

Excludes1 2

These codes carry an Excludes1 note naming Q74.3: they are not reported together with it, unless the two conditions are unrelated.

  • G72 Other and unspecified myopathies
    arthrogryposis multiplex congenita (Q74.3)
  • M20 Acquired deformities of fingers and toes
    congenital deformities and malformations of fingers and toes (Q66.-, Q68-Q70, Q74.-) names Q74.-, which includes this code

Excludes2 2

These codes carry an Excludes2 note naming Q74.3: its condition is not part of those codes, and both may be reported when the patient has both.

  • G71 Primary disorders of muscles
    arthrogryposis multiplex congenita (Q74.3)
  • G71.2 Congenital myopathies
    arthrogryposis multiplex congenita (Q74.3)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Arthrogryposis

    persistent flexure or contracture of a joint.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q74.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
754.89 Nonteratogenic anom NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q74.3Overview

What is the ICD-10 code for arthrogryposis multiplex congenita?

The ICD-10-CM code for arthrogryposis multiplex congenita is Q74.3 (sometimes written as Q743). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q74.3 (Other congenital malformations of limb(s)) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report arthrogryposis multiplex congenita on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q74.3 group to?

When arthrogryposis multiplex congenita is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q74.3 a CC or MCC?

CMS lists Q74.3 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 5 closely related codes in its exclusion list.

Is Q74.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for arthrogryposis multiplex congenita on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.