2026 ICD-10-CM Diagnosis Code Q74.3Arthrogryposis multiplex congenita

ICD-10-CM Codes›Q00-Q99›Q65-Q79›s

ICD-10-CM Q74.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q74.3 is a billable ICD-10-CM diagnosis code for arthrogryposis multiplex congenita. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q74.3
Billable Status
Yes — Valid for Submission
Code Describes
Arthrogryposis multiplex congenita
Short Description
Arthrogryposis multiplex congenita
Same as the full description in the CMS dataset.
Parent Code
Q74
Other congenital malformations of limb(s)

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategorysOther congenital malformations of limb (Q74)
This CodeQ74.3Arthrogryposis multiplex congenita

Present on Admission (POA)Billing

Q74.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adducted thumbs and arthrogryposis syndrome Christian type
  • Akinesia
  • Antenatal multi-minicore disease with arthrogryposis multiplex congenita
  • Anterior horn cell disease
  • Arthrogryposis
  • Arthrogryposis and ectodermal dysplasia syndrome
  • Arthrogryposis hyperkeratosis syndrome lethal form
  • Arthrogryposis multiplex congenita
  • Arthrogryposis with oculomotor limitation and electroretinal anomaly
  • Arthrogryposis with renal dysfunction and cholestasis syndrome
  • Autism spectrum disorder, epilepsy, arthrogryposis syndrome
  • Autosomal recessive myogenic arthrogryposis multiplex congenita
  • Congenital arthrogryposis caused by teratogen
  • Congenital flexion contracture of foot joint
  • Congenital hypoplasia of breast
  • Congenital muscular dystrophy with arthrogryposis multiplex congenita
  • Digitotalar dysmorphism
  • Distal arthrogryposis syndrome
  • Distal arthrogryposis type 10
  • Distal arthrogryposis type 3
  • Distal arthrogryposis type 4
  • Distal arthrogryposis type 5D
  • Distal arthrogryposis type 6
  • Familial arthrogryposis-cholestatic hepatorenal syndrome
  • Hepatorenal syndrome
  • Hyperpyrexia
  • Hypomyelination neuropathy arthrogryposis syndrome
  • Hypoplasia of nipple
  • Illum syndrome
  • Inherited arthrogryposis
  • Inherited disorder of bilirubin metabolism
  • Joint contracture, webbed neck, micrognathia, hypoplastic nipple syndrome
  • Kuskokwim syndrome
  • Lethal arthrogryposis with anterior horn cell disease
  • Lethal congenital contracture syndrome type 1
  • Lethal congenital contracture syndrome type 2
  • Lethal congenital contracture syndrome type 3
  • Lethal congenital contracture syndrome type 5
  • Malignant hyperthermia
  • Malignant hyperthermia with arthrogryposis and torticollis syndrome
  • Morse Rawnsley Sargent syndrome
  • Multi-core congenital myopathy
  • MYBPC1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome
  • Neck webbing
  • Neurogenic arthrogryposis multiplex congenita
  • Pelvic dysplasia, arthrogryposis of lower limbs syndrome
  • Rozin Hertz Goodman syndrome
  • Sheldon-Hall syndrome
  • X-linked distal arthrogryposis multiplex congenita
  • X-linked distal hereditary motor neuropathy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Arthrogryposis(congenital)
      • multiplex congenita
    • Guerin-Stern syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Arthrogryposis

    persistent flexure or contracture of a joint.

  • Malignant Hyperthermia

    rapid and excessive rise of temperature accompanied by muscular rigidity following general anesthesia.

  • Hepatorenal Syndrome

    functional kidney failure in patients with liver disease, usually liver cirrhosis or portal hypertension (hypertension, portal), and in the absence of intrinsic renal disease or kidney abnormality. it is characterized by intense renal vasculature constriction, reduced renal blood flow, oliguria, and sodium retention.

  • Arthrogryposis

    a rare, non-progressive congenital disorder characterized by multiple joint contractures which are present at birth.

  • Congenital Contractural Arachnodactyly|Arthrogryposis, Distal, Type 9|Beals Syndrome|CCA

    an autosomal dominant connective tissue disorder caused by mutation(s) in the fbn2 gene, encoding fibrillin-2. it is characterized by contractures, arachnodactyly, scoliosis, micrognathia, and crumpled ears.

  • Freeman-Sheldon Syndrome|Cranio-Carpo-Tarsal Syndrome|Craniocarpotarsal Dysplasia|DA2A|Distal Arthrogryposis Type 2A|Freeman Sheldon Syndrome|Whistling-Face Syndrome|Windmill-Vane-Hand Syndrome

    a rare syndrome that is inherited in an autosomal dominant or recessive pattern and caused by mutations in the myh3 gene. it is a severe form of arthrogryposis. it is characterized by the presence of distinctive facial features (small mouth, midface hypoplasia, short nose, drooping of the eyelids, deep folds in the area between the nose and the lips, and strabismus), joint deformities that lead to permanently bent fingers and toes, club foot, scoliosis, and walking difficulties.

  • TPM2 wt Allele|AMCD1|Arthrogryposis Multiplex Congenital, Distal, Type 1 Gene|DA1|DA2B|HEL-S-273|NEM4|Nemaline Myopathy Type 4 Gene|TMSB|Tropomyosin 2 (Beta) wt Allele|Tropomyosin, Skeletal Muscle Beta Gene

    human tpm2 wild-type allele is located in the vicinity of 9p13 and is approximately 9 kb in length. this allele, which encodes tropomyosin beta chain protein, is involved in muscle contraction. mutation of the gene is associated with nemaline myopathy type 4, cap myopathy type 2 and distal arthrogryposis types 1a and 2b.

  • Akinesia

    lack of movement.

  • Fetal Akinesia Deformation Sequence|FADS|Pena-Shokeir syndrome, Type 1

    a condition characterized by fetal akinesia and intrauterine growth restriction, that may be associated with mutation(s) in the rapsn or dok7 genes, encoding 43 kda receptor-associated protein of the synapse and protein dok-7, respectively.

  • Hyperpyrexia

    body temperature of 106 degrees fahrenheit (41.1 degrees celsius) or higher.

  • Malignant Hyperthermia Syndrome|Malignant Hyperpyrexia|Malignant Hyperthermia|Malignant Hyperthermia

    a rare disorder characterized by rapid rise of the body temperature, accompanied by rhabdomyolysis and, if untreated, by collapse and death. it occurs in susceptible individuals who receive certain drugs for general anesthesia, gas anesthetics, or succinylcholine. it may be inherited in an autosomal dominant pattern.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q74.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
754.89 Nonteratogenic anom NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q74.3Overview

Is Q74.3 (Other congenital malformations of limb(s)) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report arthrogryposis multiplex congenita on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q74.3 group to?

When arthrogryposis multiplex congenita is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q74.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for arthrogryposis multiplex congenita on inpatient claims.

What is the ICD-9 equivalent of Q74.3?

Under the General Equivalence Mappings, arthrogryposis multiplex congenita converts to ICD-9-CM 754.89 (nonteratogenic anom NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.