2027 ICD-10-CM Diagnosis Code Q56.1Male pseudohermaphroditism, not elsewhere classified
ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q56
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q56.1 is a billable ICD-10-CM diagnosis code for male pseudohermaphroditism, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 729 through 730. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q56.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of genital organs (Q50-Q56).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- 3-Oxo-5 alpha-steroid delta 4-dehydrogenase deficiency
- 46 XY disorder of sex development due to maternal ingestion of estrogen
- 46,XY disorder of sex development due to maternal ingestion of progestogen
- 46,XY disorder of sex development, adrenal insufficiency due to CYP11A1 deficiency
- 46,XY gonadal dysgenesis, motor and sensory neuropathy syndrome
- 46,XY ovotesticular disorder of sex development
- 46,XY partial gonadal dysgenesis
- Male pseudohermaphroditism
- Mixed sensory-motor polyneuropathy
- Motor polyneuropathy
- Ovotesticular disorder of sex development
- Rudimentary uterus in male
- Sensory polyneuropathy
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q56.1: its own notes plus those printed at Q56, block Q50-Q56, and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- 46, XY with streak gonads
- Male pseudohermaphroditism NOS
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q56.1, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
with streak gonads Q56.1
male See Also: Disorder, adrenogenital; Q56.1
cleft scrotum Q56.1
without gonadal disorder Q56.1
Rudimentary (congenital) See Also: Agenesis;
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q56.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q56.1Overview
What is the ICD-10 code for male pseudohermaphroditism, not elsewhere classified?
The ICD-10-CM code for male pseudohermaphroditism, not elsewhere classified is Q56.1 (sometimes written as Q561). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q56.1 (Indeterminate sex and pseudohermaphroditism) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report male pseudohermaphroditism, not elsewhere classified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q56.1 group to?
When male pseudohermaphroditism, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 729, 730, with relative weights from 0.6595 to 1.0553 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q56.1 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for male pseudohermaphroditism, not elsewhere classified on inpatient claims. The code appears in the Congenital malformations of genital organs (Q50-Q56) range of the CMS exempt list.
Can Q56.1 be reported with Q99.1?
Not as a rule. The Excludes1 note at Q56, which applies to Q56.1, lists "46,XX true hermaphrodite (Q99.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
