2026 ICD-10-CM Diagnosis Code Q56.1Male pseudohermaphroditism, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q56

ICD-10-CM Q56.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q56.1 is a billable ICD-10-CM diagnosis code for male pseudohermaphroditism, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 729 through 730. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q56.1
Billable Status
Yes — Valid for Submission
Code Describes
Male pseudohermaphroditism, not elsewhere classified
Short Description
Male pseudohermaphroditism, not elsewhere classified
Same as the full description in the CMS dataset.
Parent Code
Q56
Indeterminate sex and pseudohermaphroditism

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ50-Q56Congenital malformations of genital organs
CategoryQ56Indeterminate sex and pseudohermaphroditism
This CodeQ56.1Male pseudohermaphroditism, not elsewhere classified

Present on Admission (POA)Billing

Q56.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 3-Oxo-5 alpha-steroid delta 4-dehydrogenase deficiency
  • 46 XY disorder of sex development due to maternal ingestion of estrogen
  • 46,XY disorder of sex development due to maternal ingestion of progestogen
  • 46,XY disorder of sex development, adrenal insufficiency due to CYP11A1 deficiency
  • 46,XY gonadal dysgenesis, motor and sensory neuropathy syndrome
  • 46,XY ovotesticular disorder of sex development
  • 46,XY partial gonadal dysgenesis
  • Male pseudohermaphroditism
  • Mixed sensory-motor polyneuropathy
  • Motor polyneuropathy
  • Ovotesticular disorder of sex development
  • Rudimentary uterus in male
  • Sensory polyneuropathy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • 46, XY with streak gonads
  • Male pseudohermaphroditism NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Karyotype
      • 46,XY
        • with streak gonads
    • Pseudohermaphroditism
      • male
    • Pseudohermaphroditism
      • male
        • with
          • cleft scrotum
    • Pseudohermaphroditism
      • male
        • without gonadal disorder
    • Rudimentary(congenital)
      • uterus
        • in male

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q56.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
752.7 Indeterminate sex
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q56.1Overview

Is Q56.1 (Indeterminate sex and pseudohermaphroditism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report male pseudohermaphroditism, not elsewhere classified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q56.1 group to?

When male pseudohermaphroditism, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 729, 730, with relative weights from 0.6720 to 1.0587 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q56.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for male pseudohermaphroditism, not elsewhere classified on inpatient claims.

What is the ICD-9 equivalent of Q56.1?

Under the General Equivalence Mappings, male pseudohermaphroditism, not elsewhere classified converts to ICD-9-CM 752.7 (indeterminate sex). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.