2027 ICD-10-CM Diagnosis Code Q56.0Hermaphroditism, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q56

ICD-10-CM Q56.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q56.0 is a billable ICD-10-CM diagnosis code for hermaphroditism, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 729 through 730, 742 through 743, 760 through 761. The code is exempt from POA reporting. Coders also document this condition as ovotesticular disorder of sex development. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q56.0
Billable Status
Yes — Valid for Submission
Code Describes
Hermaphroditism, not elsewhere classified
Short Description
Hermaphroditism, not elsewhere classified
Same as the full description in the CMS dataset.
Parent Code
Q56
Indeterminate sex and pseudohermaphroditism

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ50-Q56Congenital malformations of genital organs
CategoryQ56Indeterminate sex and pseudohermaphroditism
This CodeQ56.0Hermaphroditism, not elsewhere classified

Present on Admission (POA)Billing

Q56.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of genital organs (Q50-Q56).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Ovotesticular disorder of sex development

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q56.0: its own notes plus those printed at Q56, block Q50-Q56, and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Ovotestis

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q56 Indeterminate sex and pseudohermaphroditism applies to 5 codes
  • 46,XX true hermaphrodite (Q99.1)
  • androgen insensitivity syndrome (E34.5-)
  • chimera 46,XX/46,XY true hermaphrodite (Q99.0)
  • female pseudohermaphroditism with adrenocortical disorder (E25.-)
  • pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
  • pure gonadal dysgenesis (Q99.1)
From Block Q50-Q56 Congenital malformations of genital organs applies to 91 codes
  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q56.0, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q56.0: they are not reported together with it, unless the two conditions are unrelated.

  • E25 Adrenogenital disorders
    indeterminate sex and pseudohermaphroditism (Q56) names Q56, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hermaphroditism

    an historical term for a variety of abnormalities in sex development that lead to anomalies in the reproductive tract and/or external genitalia.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q56.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
752.7 Indeterminate sex
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q56.0Overview

What is the ICD-10 code for hermaphroditism, not elsewhere classified?

The ICD-10-CM code for hermaphroditism, not elsewhere classified is Q56.0 (sometimes written as Q560). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q56.0 (Indeterminate sex and pseudohermaphroditism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hermaphroditism, not elsewhere classified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q56.0 group to?

When hermaphroditism, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 729, 743, 760, 761, 730, with relative weights from 0.6595 to 1.8448 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q56.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for hermaphroditism, not elsewhere classified on inpatient claims. The code appears in the Congenital malformations of genital organs (Q50-Q56) range of the CMS exempt list.

Can Q56.0 be reported with Q99.1?

Not as a rule. The Excludes1 note at Q56, which applies to Q56.0, lists "46,XX true hermaphrodite (Q99.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).