2027 ICD-10-CM Diagnosis Code Q51.4Unicornate uterus

ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q51

ICD-10-CM Q51.4
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q51.4 is a billable ICD-10-CM diagnosis code for unicornate uterus. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 742 through 743, 760 through 761. The code is exempt from POA reporting. Coders also document this condition as hemi-uterus with rudimentary cavity. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q51.4
Billable Status
Yes — Valid for Submission
Code Describes
Unicornate uterus
Short Description
Unicornate uterus
Same as the full description in the CMS dataset.
Parent Code
Congenital malformations of uterus and cervix

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ50-Q56Congenital malformations of genital organs
CategoryQ51Congenital malformations of uterus and cervix
This CodeQ51.4Unicornate uterus

Present on Admission (POA)Billing

Q51.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of genital organs (Q50-Q56).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Hemi-uterus with rudimentary cavity
  • Hemi-uterus without rudimentary cavity
  • Uterus unicornis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q51.4: its own notes plus those printed at block Q50-Q56 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Unicornate uterus with or without a separate uterine horn
  • Uterus with only one functioning horn

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Block Q50-Q56 Congenital malformations of genital organs applies to 91 codes
  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Unicornuate Uterus

    a congenital abnormality where the uterus develops with only one fallopian tube.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q51.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
752.33 Unicornuate uterus
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q51.4Overview

What is the ICD-10 code for unicornate uterus?

The ICD-10-CM code for unicornate uterus is Q51.4 (sometimes written as Q514). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q51.4 (Congenital malformations of uterus and cervix) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report unicornate uterus on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q51.4 group to?

When unicornate uterus is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 743, 760, 761, with relative weights from 0.7039 to 1.8448 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q51.4 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for unicornate uterus on inpatient claims. The code appears in the Congenital malformations of genital organs (Q50-Q56) range of the CMS exempt list.

Can Q51.4 be reported with a code from E34.5?

Not as a rule. The Excludes1 note at block Q50-Q56, which applies to Q51.4, lists "androgen insensitivity syndrome (E34.5-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).