2026 ICD-10-CM Diagnosis Code I89.0Lymphedema, not elsewhere classified

ICD-10-CM Codes›I00–I99›I80-I89›I89

ICD-10-CM I89.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I89.0 is a billable ICD-10-CM diagnosis code for lymphedema, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified diseases of veins and lymphatics.

Code Identity

ICD-10-CM Code
I89.0
Billable Status
Yes — Valid for Submission
Code Describes
Lymphedema, not elsewhere classified
Short Description
Lymphedema, not elsewhere classified
Same as the full description in the CMS dataset.
Parent Code
I89
Other noninfective disorders of lymphatic vessels and lymph nodes

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI80-I89Diseases of veins, lymphatic vessels and lymph nodes, not elsewhere classified
CategoryI89Other noninfective disorders of lymphatic vessels and lymph nodes
This CodeI89.0Lymphedema, not elsewhere classified

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired cutaneous lymphangiectasia
  • Acquired lymphangiectasia
  • Acquired lymphangiectasia with chylous reflux
  • Acquired lymphedema of lower extremity
  • Bilateral lower limb edema
  • Bilateral upper limb edema
  • Cholestasis in newborn
  • Cholestasis-edema syndrome, Norwegian type
  • Chronic acquired lymphedema
  • Chronic disease of lymphatic vessels
  • Congenital lymphangiectasia
  • Dependent lymphedema
  • Dependent lymphedema due to impaired mobility
  • Edema of left upper limb
  • Edema of male genital organs
  • Edema of oral soft tissues
  • Edema of penis
  • Edema of right upper limb
  • Edema of scrotum
  • Edema of upper arm
  • Elephantiasis neurofibromatosa
  • Facial lymphedema due to acne
  • Facial lymphedema due to rosacea
  • Hereditary disorder of lymphatic system
  • Iatrogenic lymphedema
  • Infectious edema
  • Intestinal lymphangiectasis
  • Jugular lymphatic obstruction sequence
  • Lipedema
  • Lipo-lymphedema
  • Lymphedema
  • Lymphedema associated with obesity
  • Lymphedema due to and following radiotherapy
  • Lymphedema due to chronic inflammation
  • Lymphedema due to endocrine disease
  • Lymphedema due to infection
  • Lymphedema due to inflammatory disease
  • Lymphedema due to lymphogranuloma venereum
  • Lymphedema due to malignant infiltration
  • Lymphedema due to podoconiosis
  • Lymphedema due to radiation
  • Lymphedema due to recurrent infection
  • Lymphedema due to trauma
  • Lymphedema due to venous disease
  • Lymphedema due to venous insufficiency
  • Lymphedema hypoparathyroidism syndrome
  • Lymphedema of bilateral lower limbs
  • Lymphedema of bilateral upper limbs
  • Lymphedema of ear
  • Lymphedema of genitalia
  • Lymphedema of left lower limb
  • Lymphedema of left upper limb
  • Lymphedema of limb
  • Lymphedema of limbs due to immobility, chronic dependency and/or venous insufficiency
  • Lymphedema of lip
  • Lymphedema of lower extremity
  • Lymphedema of penis
  • Lymphedema of right lower limb
  • Lymphedema of right upper limb
  • Lymphedema of scrotum
  • Lymphedema of uncertain etiology
  • Lymphedema of upper arm
  • Lymphedema of upper limb
  • Lymphedema praecox
  • Lymphedema, atrial septal defect, facial changes syndrome
  • Lymphedematous hyperkeratosis
  • Lymphovenous edema
  • Mullerian remnant
  • Neurofibromatosis type 1
  • Obliteration of lymphatic vessel
  • Onchocercal elephantiasis
  • Persistent Mullerian derivative with lymphangiectasia and polydactyly syndrome
  • Podoconiosis
  • Postsurgical lymphedema
  • Primary lymphangiectasis of intestine
  • Primary lymphedema
  • Primary lymphedema with systemic and visceral involvement
  • Primary lymphedema with systemic involvement
  • Primary lymphedema with visceral involvement
  • Secondary intestinal lymphangiectasia
  • Secondary pediatric lymphedema
  • Secondary xanthomatous infiltration of the skin
  • Syndromic primary lymphedema
  • Xanthoma due to lymphedema

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Elephantiasis (nonfilarial) NOS
  • Lymphangiectasis
  • Obliteration, lymphatic vessel
  • Praecox lymphedema
  • Secondary lymphedema

Type 1 Excludes

  • postmastectomy lymphedema I97.2

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Compression
      • lymphatic vessel
    • Dilatation
      • lymphatic vessel
    • Edema, edematous(infectious) (pitting) (toxic)
      • due to
        • lymphatic obstruction
    • Edema, edematous(infectious) (pitting) (toxic)
      • lymphatic
    • Elephantiasis(nonfilarial)
    • Elephantiasis(nonfilarial)
      • glandular
    • Elephantiasis(nonfilarial)
      • lymphangiectatic
    • Elephantiasis(nonfilarial)
      • lymphatic vessel
    • Elephantiasis(nonfilarial)
      • scrotum (nonfilarial)
    • Elephantiasis(nonfilarial)
      • streptococcal
    • Elephantiasis(nonfilarial)
      • telangiectodes
    • Lymphangiectasis
    • Lymphangiectasis
      • postinfectional
    • Lymphangiectasis
      • scrotum
    • Lymphangiectatic elephantiasis, nonfilarial
    • Lymphectasia
    • Lymphedema(acquired)
      • praecox
    • Lymphedema(acquired)
      • secondary
    • Obliteration
      • lymphatic vessel
    • Obstruction, obstructed, obstructive
      • lymphatic
    • Obstruction, obstructed, obstructive
      • thoracic duct
    • Occlusion, occluded
      • lymph or lymphatic channel
    • Occlusion, occluded
      • thoracic duct

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR039
Other specified diseases of veins and lymphatics
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Breast Cancer Lymphedema

    abnormal accumulation of lymph in the arm, shoulder and breast area associated with surgical treatment (e.g., mastectomy) or radiation treatment of breast cancer.

  • Lymphedema

    edema due to obstruction of lymph vessels or disorders of the lymph nodes.

  • Non-Filarial Lymphedema

    a form of elephantiasis caused by soil particles which penetrate the skin of the foot. it is limited to tropical regions with soils of high volcanic content.

  • Yellow Nail Syndrome

    a rare condition characterized by the presence of yellow nails, lymphedema, and/or pleural effusion with respiratory tract involvement. abnormal lymphatic network may play a role in its etiology. occasionally inherited, yellow nail syndrome mostly is sporadic without apparent family history.

  • Lipedema

    disorder of adipose tissue characterized by symmetric and bilateral enlargement of the lower extremities due to abnormal deposition of subcutaneous fat often in obese women. it is associated with hematoma, pain and may progress to secondary lymphedema which is known as lipolymphedema.

  • Mastectomy

    surgical procedure to remove one or both breasts.

  • Primary Lymphedema

    a congenital condition that results in swelling in the arms or legs, and can occur during adolescence or adulthood. loss of motion and pain may also accompany the swelling. protein-rich lymphatic fluid accumulates in tissues, engorging and enlarging vessels and often causing visible swelling, tenderness, and pain. left untreated, the affected tissues may continue to swell, and can become hardened or fibrotic and susceptible to infection.

Patient EducationClinical

Lymphedema

Lymphedema is the name of a type of swelling. It happens when lymph builds up in your body's soft tissues. Lymph is a fluid that contains white blood cells that defend against germs. It can build up when the lymph system is damaged or blocked. It usually happens in the arms or legs.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I89.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
457.1 Other lymphedema
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I89.0Overview

Is I89.0 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lymphedema, not elsewhere classified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does I89.0 group to?

When lymphedema, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I89.0?

Under the General Equivalence Mappings, lymphedema, not elsewhere classified converts to ICD-9-CM 457.1 (other lymphedema). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.