2027 ICD-10-CM Diagnosis Code I89.0Lymphedema, not elsewhere classified
ICD-10-CM Codes›I00–I99›I80-I89›I89
- Billable — Valid for Submission
- Chronic Condition
I89.0 is a billable ICD-10-CM diagnosis code for lymphedema, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified diseases of veins and lymphatics.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acquired cutaneous lymphangiectasia
- Acquired lymphangiectasia
- Acquired lymphangiectasia with chylous reflux
- Acquired lymphedema of lower extremity
- Bilateral lower limb edema
- Bilateral upper limb edema
- Cholestasis in newborn
- Cholestasis-edema syndrome, Norwegian type
- Chronic acquired lymphedema
- Chronic disease of lymphatic vessels
- Congenital lymphangiectasia
- Cutaneous papillomatosis
- Dependent lymphedema
- Dependent lymphedema due to impaired mobility
- Edema of left upper limb
- Edema of male genital organs
- Edema of oral soft tissues
- Edema of penis
- Edema of right upper limb
- Edema of scrotum
- Edema of upper arm
- Elephantiasis neurofibromatosa
- Elephantiasis nostra verrucosa
- Facial lymphedema due to acne
- Facial lymphedema due to rosacea
- Hereditary disorder of lymphatic system
- Hyperkeratosis due to lymphedema
- Iatrogenic lymphedema
- Infectious edema
- Intestinal lymphangiectasis
- Jugular lymphatic obstruction sequence
- Lipedema
- Lipo-lymphedema
- Lymphedema
- Lymphedema associated with obesity
- Lymphedema caused by ionizing radiation
- Lymphedema due to and following radiotherapy
- Lymphedema due to chronic inflammation
- Lymphedema due to endocrine disease
- Lymphedema due to infection
- Lymphedema due to inflammatory disease
- Lymphedema due to lymphogranuloma venereum
- Lymphedema due to malignant infiltration
- Lymphedema due to recurrent infection
- Lymphedema due to trauma
- Lymphedema due to venous disease
- Lymphedema due to venous insufficiency
- Lymphedema following axillary lymphadenectomy
- Lymphedema following iliac lymphadenectomy
- Lymphedema following inguinal lymphadenectomy
- Lymphedema following pelvic lymphadenectomy
- Lymphedema hypoparathyroidism syndrome
- Lymphedema of bilateral lower limbs
- Lymphedema of bilateral upper limbs
- Lymphedema of ear
- Lymphedema of genitalia
- Lymphedema of intestine
- Lymphedema of left lower limb
- Lymphedema of left upper limb
- Lymphedema of limb
- Lymphedema of limbs due to immobility, chronic dependency and/or venous insufficiency
- Lymphedema of lip
- Lymphedema of lower extremity
- Lymphedema of penis
- Lymphedema of right lower limb
- Lymphedema of right upper limb
- Lymphedema of scrotum
- Lymphedema of uncertain etiology
- Lymphedema of upper arm
- Lymphedema of upper limb
- Lymphedema praecox
- Lymphedema, atrial septal defect, facial changes syndrome
- Lymphovenous edema
- Mullerian remnant
- Neurofibromatosis type 1
- Non-filarial elephantiasis
- Obliteration of lymphatic vessel
- Onchocercal elephantiasis
- Papillomatosis due to lymphedema
- Persistent Mullerian derivative with lymphangiectasia and polydactyly syndrome
- Podoconiosis
- Postsurgical lymphedema
- Primary lymphangiectasis of intestine
- Primary lymphedema
- Primary lymphedema with systemic and visceral involvement
- Primary lymphedema with systemic involvement
- Primary lymphedema with visceral involvement
- Secondary intestinal lymphangiectasia
- Secondary pediatric lymphedema
- Secondary xanthomatous infiltration of the skin
- Syndromic primary lymphedema
- Xanthoma due to lymphedema
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to I89.0: its own notes plus those printed at I89 and Chapter 9. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Elephantiasis (nonfilarial) NOS
- Lymphangiectasis
- Obliteration, lymphatic vessel
- Praecox lymphedema
- Secondary lymphedema
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- postmastectomy lymphedema (I97.2)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- systemic connective tissue disorders (M30-M36)
- transient cerebral ischemic attacks and related syndromes (G45.-)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name I89.0, its category, or a range that includes it.
Use Additional Code 1
These codes say to use an additional code from the note, and I89.0 is one of the codes named.
- Q93.52 Phelan-McDermid syndromelymphedema (I89.0)
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
lymphatic vessel I89.0
lymphatic vessel I89.0
Elephantiasis (nonfilarial) I89.0
glandular I89.0
lymphangiectatic I89.0
lymphatic vessel I89.0
scrotum (nonfilarial) I89.0
streptococcal I89.0
telangiectodes I89.0
Lymphangiectasis I89.0
postinfectional I89.0
scrotum I89.0
Lymphectasia I89.0
Lymphedema (acquired) See Also: Elephantiasis;
lymphatic vessel I89.0
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Lymphedema
edema due to obstruction of lymph vessels or disorders of the lymph nodes.
Patient EducationClinical
Lymphedema
Lymphedema is the name of a type of swelling. It happens when lymph builds up in your body's soft tissues. Lymph is a fluid that contains white blood cells that defend against germs. It can build up when the lymph system is damaged or blocked. It usually happens in the arms or legs.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert I89.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About I89.0Overview
What is the ICD-10 code for lymphedema, not elsewhere classified?
The ICD-10-CM code for lymphedema, not elsewhere classified is I89.0 (sometimes written as I890). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is I89.0 a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report lymphedema, not elsewhere classified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does I89.0 group to?
When lymphedema, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Can I89.0 be reported with I97.2?
Not as a rule. The Excludes1 note on I89.0 lists "postmastectomy lymphedema (I97.2)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of I89.0?
Under the General Equivalence Mappings, lymphedema, not elsewhere classified converts to ICD-9-CM 457.1 (other lymphedema). The mapping is a direct match.
