2027 ICD-10-CM Diagnosis Code I01Rheumatic fever with heart involvement

ICD-10-CM Codes›I00–I99›I00-I02›I01

ICD-10-CM I01
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

I01 is a non-billable ICD-10-CM category code for rheumatic fever with heart involvement, so it cannot be submitted on claims. Use a more specific code from this category instead, such as I01.0, I01.1, I01.2, and I01.8.

Code Identity

ICD-10-CM Code
I01
Billable Status
No — Non-Billable Category
Code Describes
Rheumatic fever with heart involvement
Short Description
Rheumatic fever with heart involvement
Same as the full description in the CMS dataset.
Chapter
I00-I02
Acute rheumatic fever

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI00-I02Acute rheumatic fever
CategoryI01Rheumatic fever with heart involvement
This CodeI01Rheumatic fever with heart involvement

Specific Coding for Rheumatic fever with heart involvementOverview

Non-specific codes like I01 require more characters. Use one of these billable codes instead:

  • Use I01.0 for Acute rheumatic pericarditis

  • Use I01.1 for Acute rheumatic endocarditis

  • Use I01.2 for Acute rheumatic myocarditis

  • Use I01.8 for Other acute rheumatic heart disease

  • Use I01.9 for Acute rheumatic heart disease, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to I01: its own notes plus those printed at Chapter 9. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 9 (I00-I99) Diseases of the circulatory system applies to 1,433 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name I01, its category, or a range that includes it.

Applicable To 1

These notes mention I01.

  • I02.0 Rheumatic chorea with heart involvement
    Rheumatic chorea with heart involvement of any type classifiable under I01.-

Excludes2 1

These codes carry an Excludes2 note naming I01: its condition is not part of those codes, and both may be reported when the patient has both.

  • I51 Complications and ill-defined descriptions of heart disease
    heart disease specified as rheumatic (I00-I09) names I00-I09, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Patient EducationClinical

Streptococcal Infections

Strep is short for Streptococcus, a type of bacteria that often lives in your nose and throat. Most strep infections are mild, but some may become serious depending on your overall health.

The full article covers:

  • What are streptococcal infections?
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  • What are the symptoms of streptococcal infections?
  • How are streptococcal infections diagnosed?
  • What are the treatments for streptococcal infections?
  • Can streptococcal infections be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About I01Overview

What is the ICD-10 code for rheumatic fever with heart involvement?

I01 is the ICD-10-CM category for rheumatic fever with heart involvement, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is I01 (Rheumatic fever with heart involvement) a billable code?

No. This is a category header that groups the codes for rheumatic fever with heart involvement, and headers cannot be submitted on claims. Claims for rheumatic fever with heart involvement need a more specific code from this category, such as I01.0, I01.1, and I01.2.