2026 ICD-10-CM Diagnosis Code I01Rheumatic fever with heart involvement

ICD-10-CM Codes›I00–I99›I00-I02›I01

ICD-10-CM I01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I01 is a non-billable ICD-10-CM category code for rheumatic fever with heart involvement, so it cannot be submitted on claims. Use a more specific code from this category instead, such as I01.0, I01.1, I01.2, and I01.8.

Code Identity

ICD-10-CM Code
I01
Billable Status
No — Non-Billable Category
Code Describes
Rheumatic fever with heart involvement
Short Description
Rheumatic fever with heart involvement
Same as the full description in the CMS dataset.
Chapter
I00-I02
Acute rheumatic fever

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI00-I02Acute rheumatic fever
CategoryI01Rheumatic fever with heart involvement
This CodeI01Rheumatic fever with heart involvement

Specific Coding for Rheumatic fever with heart involvementOverview

Non-specific codes like I01 require more characters. Use one of these billable codes instead:

  • Use I01.0 for Acute rheumatic pericarditis

  • Use I01.1 for Acute rheumatic endocarditis

  • Use I01.2 for Acute rheumatic myocarditis

  • Use I01.8 for Other acute rheumatic heart disease

  • Use I01.9 for Acute rheumatic heart disease, unspecified

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • chronic diseases of rheumatic origin I05 I09

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Patient EducationClinical

Streptococcal Infections

Strep is short for Streptococcus, a type of bacteria. There are several types. Two of them cause most of the strep infections in people: group A and group B.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I01Overview

What is the ICD-10 code for rheumatic fever with heart involvement?

I01 is the ICD-10-CM category for rheumatic fever with heart involvement, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is I01 (Rheumatic fever with heart involvement) a billable code?

No. This is a category header that groups the codes for rheumatic fever with heart involvement, and headers cannot be submitted on claims. Claims for rheumatic fever with heart involvement need a more specific code from this category, such as I01.0, I01.1, and I01.2.