2026 ICD-10-CM Diagnosis Code I01Rheumatic fever with heart involvement

ICD-10-CM Codes›I00–I99›I00-I02›I01

ICD-10-CM I01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I01 is a non-billable ICD-10-CM category code for rheumatic fever with heart involvement, so it cannot be submitted on claims. Use a more specific code from this category instead, such as I01.0, I01.1, I01.2, and I01.8.

Code Identity

ICD-10-CM Code
I01
Billable Status
No — Non-Billable Category
Code Describes
Rheumatic fever with heart involvement
Chapter
I00-I02
Acute rheumatic fever

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI00-I02Acute rheumatic fever
CategoryI01Rheumatic fever with heart involvement
This CodeI01Rheumatic fever with heart involvement

Specific Coding for Rheumatic fever with heart involvementOverview

Non-specific codes like I01 require more characters. Use one of these billable codes instead:

  • Use I01.0 for Acute rheumatic pericarditis

  • Use I01.1 for Acute rheumatic endocarditis

  • Use I01.2 for Acute rheumatic myocarditis

  • Use I01.8 for Other acute rheumatic heart disease

  • Use I01.9 for Acute rheumatic heart disease, unspecified

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • chronic diseases of rheumatic origin I05 I09

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Fever(inanition) (of unknown origin) (persistent) (with chills) (with rigor)
      • rheumatic (active) (acute) (chronic) (subacute)
        • active with heart involvement

Patient EducationClinical

Streptococcal Infections

Strep is short for Streptococcus, a type of bacteria. There are several types. Two of them cause most of the strep infections in people: group A and group B.

Read the full article at MedlinePlus

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Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I01Overview

Is I01 (Rheumatic fever with heart involvement) a billable code?

No. This is a category header that groups the codes for rheumatic fever with heart involvement, and headers cannot be submitted on claims. Claims for rheumatic fever with heart involvement need a more specific code from this category, such as I01.0, I01.1, and I01.2.