Rheumatic fever without heart involvement (I00) ICD-10-CM
The I00 code range covers rheumatic fever without heart involvement with 1 ICD-10-CM diagnosis codes. 1 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- arthritis, rheumatic, acute or subacute
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the I00 Range 1 codes · 1 billable
- I00 Rheumatic fever without heart involvement
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the I00 range.
Rheumatic Fever
A febrile disease occurring as a delayed sequela of infections with STREPTOCOCCUS PYOGENES. It is characterized by multiple focal inflammatory lesions of the connective tissue structures, such as the heart, blood vessels, and joints (POLYARTHRITIS) and brain, and by the presence of ASCHOFF BODIES in the myocardium and skin.
About the I00 Code Range
The ICD-10 code I00 is used to classify rheumatic fever without heart involvement, a condition where systemic inflammation occurs due to a prior streptococcal infection but the heart is not affected. This code specifically captures cases of acute rheumatic fever presenting without cardiac complications.
This coding applies to conditions such as migratory polyarthritis, subacute rheumatic arthritis, and erythema marginatum—all recognized synonyms or related manifestations of rheumatic fever when the heart remains uninvolved. Using ICD-10 code I00 helps healthcare professionals accurately document and report cases of acute rheumatic fever where symptoms such as joint inflammation, skin rash, or pneumonitis occur without signs of rheumatic heart disease. This distinction is important for proper diagnosis, treatment planning, and epidemiological tracking. Including synonyms like recurrent rheumatic fever and subacute arthropathy supports coders in linking common terms with the official code, ensuring precise medical record-keeping.
Questions About This Page
How many billable codes are in the I00 range?
Of the 1 codes in this range, 1 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the I00 range classify?
The range classifies rheumatic fever without heart involvement. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
