Rheumatic fever with heart involvement (I01) ICD-10-CM
The I01 code range covers rheumatic fever with heart involvement with 6 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the I01 Range 6 codes · 5 billable
About the I01 Code Range
ICD-10 codes I01 and its subcodes are used to classify cases of rheumatic fever with heart involvement. These codes specifically identify different types of acute rheumatic heart disease affecting the heart's layers, including the pericardium, endocardium, and myocardium.
These codes help healthcare providers document and code conditions such as acute rheumatic pericarditis (I01.0), known also as acute rheumatic heart disease or acute rheumatic fever affecting the pericardium; acute rheumatic endocarditis (I01.1), which includes acute rheumatic carditis and valvulitis affecting the heart’s inner lining; and acute rheumatic myocarditis (I01.2), which impacts the heart muscle itself. The section also covers other acute rheumatic heart diseases (I01.8), such as pancarditis including MacCallum’s patch, and unspecified acute rheumatic heart disease (I01.9). Using these specific codes ensures accurate identification of rheumatic fever’s cardiac manifestations, supporting clinical decisions and medical billing. This section is essential when searching for the ICD-10 code for rheumatic fever with heart involvement and its variants.
Questions About This Page
How many billable codes are in the I01 range?
Of the 6 codes in this range, 5 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the I01 range classify?
The range classifies rheumatic fever with heart involvement. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
