Rheumatic fever with heart involvement (I01) ICD-10-CM
The I01 code range covers rheumatic fever with heart involvement with 6 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the I01 Range 6 codes · 5 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the I01 range.
Acute Rheumatic Endocarditis
Inflammation of the endocardium in acute rheumatic heart disease.
Acute Rheumatic Heart Disease
Pancarditis, involving inflammation of the endocardium, myocardium, and epicardium. It results from an autoimmune reaction following an infection with Streptococcus pyogenes (Group A Streptococci).
Acute Rheumatic Myocarditis
Inflammation of the myocardium in acute rheumatic heart disease.
Acute Rheumatic Pericarditis
Inflammation of the pericardium in acute rheumatic heart disease.
About the I01 Code Range
Acute rheumatic fever can involve the sac around the heart, the heart’s inner lining, or the heart muscle.
The subdivisions separate inflammation of the sac around the heart (I01.0), the inner lining (I01.1), and the heart muscle (I01.2). They also include other acute rheumatic heart disease (I01.8) and acute rheumatic heart disease that is unspecified (I01.9).
Questions About This Page
How many billable codes are in the I01 range?
Of the 6 codes in this range, 5 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the I01 range classify?
The range classifies rheumatic fever with heart involvement. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
