2026 ICD-10-CM Diagnosis Code G93.44Adult-onset leukodystrophy with axonal spheroids

ICD-10-CM Codes›G00–G99›G89-G99›G93

ICD-10-CM G93.44
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G93.44 is a billable ICD-10-CM diagnosis code for adult-onset leukodystrophy with axonal spheroids. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 974 through 976. The code is restricted by the Medicare Code Editor to adult patients (age 15 through 124). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G93.44
Billable Status
Yes — Valid for Submission
Code Describes
Adult-onset leukodystrophy with axonal spheroids
Short Description
Adult-onset leukodystrophy with axonal spheroids
Same as the full description in the CMS dataset.
Parent Code
G93.4
Other and unspecified encephalopathy

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG89-G99Other disorders of the nervous system
CategoryG93Other disorders of brain
This CodeG93.44Adult-onset leukodystrophy with axonal spheroids

Code EditsBilling

Medicare Code Editor checks that affect claim validity for G93.44.

Adult diagnoses
The Medicare Code Editor detects inconsistencies in adult cases by checking a patient's age and any diagnosis on the patient's record. The adult code edits apply to patients age range is 15–124 years inclusive (e.g., senile delirium, mature cataract).

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Adult-onset leukoencephalopathy with axonal spheroids and pigmented glia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Leukoencephalopathy
      • adult-onset, with axonal spheroids (and pigmented glia)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement G93.44 replaces the following previously assigned code(s):

  • G93.49 - Other encephalopathy
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G93.44Overview

Is G93.44 (Other and unspecified encephalopathy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report adult-onset leukodystrophy with axonal spheroids on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does G93.44 group to?

When adult-onset leukodystrophy with axonal spheroids is the principal diagnosis on an inpatient stay, it groups to MS-DRG 974, 975, 976, with relative weights from 0.8945 to 2.8860 depending on complications. Higher weights mean higher Medicare reimbursement.

Who can G93.44 be reported for?

The Medicare Code Editor checks adult-onset leukodystrophy with axonal spheroids against patient demographics: this code is intended for adult patients (age 15 through 124). Claims outside these limits are flagged as inconsistent.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.