2027 ICD-10-CM Diagnosis Code E56.1Deficiency of vitamin K

ICD-10-CM Codes›E00–E89›E50-E64›E56

ICD-10-CM E56.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

E56.1 is a billable ICD-10-CM diagnosis code for deficiency of vitamin K. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 640 through 641. Coders also document this condition as deficiency of vitamin K1. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nutritional deficiencies.

Code Identity

ICD-10-CM Code
E56.1
Billable Status
Yes — Valid for Submission
Code Describes
Deficiency of vitamin K
Short Description
Deficiency of vitamin K
Same as the full description in the CMS dataset.
Parent Code
E56
Other vitamin deficiencies

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE50-E64Other nutritional deficiencies
CategoryE56Other vitamin deficiencies
This CodeE56.1Deficiency of vitamin K

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Deficiency of vitamin K1
  • Deficiency of vitamin K2
  • Disorder of vitamin K
  • Disorder of vitamin K1
  • Disorder of vitamin K2
  • Inadequate intake of vitamin K and/or vitamin K derivative
  • Vitamin K below reference range
  • Vitamin K deficiency
  • Vitamin K1 below reference range
  • Vitamin K2 below reference range

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to E56.1: its own notes plus those printed at E56, block E50-E64, and Chapter 4. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

On E56.1 itself
  • deficiency of coagulation factor due to vitamin K deficiency (D68.4)
  • vitamin K deficiency of newborn (P53)
From E56 Other vitamin deficiencies applies to 4 codes
  • sequelae of other vitamin deficiencies (E64.8)
From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Block E50-E64 Other nutritional deficiencies applies to 50 codes

Notes

General instructions on how these codes are used.

From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name E56.1, its category, or a range that includes it.

Applicable To 1

These notes mention E56.1.

  • P00.4 Newborn affected by maternal nutritional disorders
    Newborn affected by maternal disorders classifiable to E40-E64 names E40-E64, which includes this code

Excludes1 3

These codes carry an Excludes1 note naming E56.1: they are not reported together with it, unless the two conditions are unrelated.

  • T45.7X6 Underdosing of anticoagulant antagonist, vitamin K and other coagulants
    vitamin K deficiency (E56.1)
  • T45.2X6 Underdosing of vitamins
    vitamin deficiencies (E50-E56) names E50-E56, which includes this code
  • Z72.4 Inappropriate diet and eating habits
    malnutrition and other nutritional deficiencies (E40-E64) names E40-E64, which includes this code

Code First 2

These codes say to code first a condition named in the note, and E56.1 is one of the conditions named.

  • G99.8 Other specified disorders of nervous system in diseases classified elsewhere
    avitaminosis (E56.-) names E56.-, which includes this code
  • G63 Polyneuropathy in diseases classified elsewhere
    nutritional deficiency (E40-E64) names E40-E64, which includes this code

Notes 1

These notes mention E56.1.

  • E64 Sequelae of malnutrition and other nutritional deficiencies
    This category is to be used to indicate conditions in categories E43, E44, E46, E50-E63 as the cause of sequelae, which are themselves classified elsewhere. The 'sequelae' include conditions specified as such; they also include the late effects of diseases classifiable to the above categories if the disease itself is no longer present names E50-E63, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END007
Nutritional deficiencies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Malnutrition

Malnutrition means that your body isn't getting enough calories or the right balance of nutrients to stay healthy. This can happen if you don't get enough protein, carbohydrates, and fats, eat too much unhealthy food, or don't get the vitamins and minerals your body needs.

The full article covers:

  • What is malnutrition?
  • What are the types of malnutrition?
  • What causes malnutrition?
  • Who is at risk for developing malnutrition?
  • What are the symptoms of malnutrition?
  • How is malnutrition diagnosed?
  • What are the treatments for malnutrition?
  • Can malnutrition be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E56.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
269.0 Deficiency of vitamin k
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About E56.1Overview

What is the ICD-10 code for deficiency of vitamin K?

The ICD-10-CM code for deficiency of vitamin K is E56.1 (sometimes written as E561). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is E56.1 (Other vitamin deficiencies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report deficiency of vitamin K on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does E56.1 group to?

When deficiency of vitamin K is the principal diagnosis on an inpatient stay, it groups to MS-DRG 641, 640, with relative weights from 0.7864 to 1.3392 depending on complications. Higher weights mean higher Medicare reimbursement.

Can E56.1 be reported with D68.4?

Not as a rule. The Excludes1 note on E56.1 lists "deficiency of coagulation factor due to vitamin K deficiency (D68.4)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of E56.1?

Under the General Equivalence Mappings, deficiency of vitamin K converts to ICD-9-CM 269.0 (deficiency of vitamin k). The mapping is a direct match.