2026 ICD-10-CM Diagnosis Code D47.02Systemic mastocytosis
ICD-10-CM Codes›C00–D49›D37-D48›D47
- Billable — Valid for Submission
- Not Chronic
D47.02 is a billable ICD-10-CM diagnosis code for systemic mastocytosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 820 through 825, 840 through 842. Coders also document this condition as indolent systemic mastocytosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neoplasms of unspecified nature or uncertain behavior.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Malignant mastocytosis
- Smoldering systemic mastocytosis
- Systemic mast cell disease
- Systemic mastocytosis with associated clonal hematological non-mast cell lineage disease
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Indolent systemic mastocytosis
- Isolated bone marrow mastocytosis
- Smoldering systemic mastocytosis
- Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
- , if applicable, any associated hematological non-mast cell lineage disease, such as:
- acute myeloid leukemia C92.6 C92.A
- chronic myelomonocytic leukemia C93.1
- essential thrombocytosis D47.3
- hypereosinophilic syndrome D72.1
- myelodysplastic syndrome D46.9
- myeloproliferative syndrome D47.1
- non-Hodgkin lymphoma C82 C85
- plasma cell myeloma C90.0
- polycythemia vera D45
Type 1 Excludes
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Disease, diseased - See Also: Syndrome;
- systemic tissue mast cell - D47.02
- disease, systemic tissue - D47.02
- Mastocytosis - D47.09
- indolent systemic - D47.02
- isolated bone marrow - D47.02
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Disease, diseased
- systemic tissue mast cell
- Mast cell
- disease, systemic tissue
- Mastocytosis
- indolent systemic
- Mastocytosis
- isolated bone marrow
- Mastocytosis
- systemic (indolent) (smoldering)
- with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Smoldering Systemic Mastocytosis
slowly progressive systemic mastocytosis with uncertain prognosis. it is characterized by organomegaly and absence of aggressive disease.Smoldering Systemic Mastocytosis with an Associated Myeloid Neoplasm|Smoldering Systemic Mastocytosis with an Associated Hematologic Neoplasm
smoldering systemic mastocytosis associated with the presence of a clonal non-mast cell myeloid neoplasm (e.g., myelodysplastic syndrome, myeloproliferative neoplasm, and acute myeloid leukemia).
Patient EducationClinical
Systemic mastocytosis
Systemic mastocytosis is a blood disorder that can affect many different body systems. Individuals with the condition can develop signs and symptoms at any age, but it usually appears after adolescence.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert D47.02 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code History & ChangesHistory
Replacement D47.02 replaces the following previously assigned code(s):
- D47.0 - Histiocytic and mast cell tumors of uncertain behavior
- D47.0 - Mast cell neoplasms of uncertain behavior
Questions About D47.02Overview
Is D47.02 (Mast cell neoplasms of uncertain behavior) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report systemic mastocytosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does D47.02 group to?
When systemic mastocytosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 820, 821, 822, 823, 824, 825, 840, 841, 842, with relative weights from 1.0104 to 5.8648 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of D47.02?
Under the General Equivalence Mappings, systemic mastocytosis converts to ICD-9-CM 238.5 (mastocytoma NOS). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
