2026 ICD-10-CM Diagnosis Code D33.3Benign neoplasm of cranial nerves

ICD-10-CM CodesC00–D49D10-D36D33

ICD-10-CM D33.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D33.3 is a billable ICD-10-CM diagnosis code for benign neoplasm of cranial nerves. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.

Code Identity

ICD-10-CM Code
D33.3
Billable Status
Yes — Valid for Submission
Code Describes
Benign neoplasm of cranial nerves
Short Description
Benign neoplasm of cranial nerves
Same as the full description in the CMS dataset.
Parent Code
Benign neoplasm of brain and other parts of central nervous system

Code Classification

ChapterC00–D49Neoplasms
SectionD10-D36Benign neoplasms, except benign neuroendocrine tumors
CategoryD33Benign neoplasm of brain and other parts of central nervous system
This CodeD33.3Benign neoplasm of cranial nerves

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acoustic neuroma
  • Acoustic neuroma of bilateral vestibular nerves
  • Acoustic neuroma of left vestibular nerve
  • Acoustic neuroma of right vestibular nerve
  • Benign neoplasm of abducens nerve
  • Benign neoplasm of accessory nerve
  • Benign neoplasm of cranial nerve
  • Benign neoplasm of facial nerve
  • Benign neoplasm of glossopharyngeal nerve
  • Benign neoplasm of hypoglossal nerve
  • Benign neoplasm of oculomotor nerve
  • Benign neoplasm of olfactory nerve
  • Benign neoplasm of olfactory tract
  • Benign neoplasm of optic nerve
  • Benign neoplasm of optic nerve and nerve sheath
  • Benign neoplasm of trigeminal nerve
  • Benign neoplasm of trochlear nerve
  • Benign neoplasm of vagus nerve
  • Benign neoplasm of vestibulocochlear nerve
  • Bilateral vestibular neuropathy
  • Cellular schwannoma
  • Cerebellopontine angle syndrome
  • Disorder of bilateral acoustic nerves
  • Disorder of left labyrinth due to schwannoma
  • Disorder of left vestibular nerve
  • Disorder of olfactory nerve
  • Disorder of right labyrinth due to schwannoma
  • Disorder of right vestibular nerve
  • Melanocytoma of optic nerve head
  • Meningioma of optic nerve sheath
  • Meningioma of orbit
  • Neoplasm of abducens nerve
  • Neoplasm of accessory nerve
  • Neoplasm of facial nerve
  • Neoplasm of glossopharyngeal nerve
  • Neoplasm of hypoglossal nerve
  • Neoplasm of oculomotor nerve
  • Neoplasm of olfactory nerve
  • Neoplasm of trigeminal nerve
  • Neoplasm of trochlear nerve
  • Neoplasm of vagus nerve
  • Schwannoma of cranial nerve
  • Schwannoma of nerve of face
  • Trigeminal schwannoma

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Benign neoplasm of olfactory bulb

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Neurilemmoma
      • acoustic (nerve)
    • Neuroma
      • acoustic (nerve)
    • Neuroma
      • optic (nerve)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO073
Benign neoplasms
Default principal diagnosis: inpatient Yes · outpatient Yes

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary
Malig.
Secondary
Ca
in situ
BenignUncertainUnspec.
acoustic nerveC72.4C79.49D33.3D43.3D49.7
auditory nerveC72.4C79.49D33.3D43.3D49.7
chiasma opticumC72.3C79.49D33.3D43.3D49.7
cranial (fossa, any) nerveC72.50C79.49D33.3D43.3D49.7
cranial (fossa, any) nerve specified NECC72.59C79.49D33.3D43.3D49.7
ganglia [See Also: Neoplasm, nerve, peripheral] cranial nerveC72.50C79.49D33.3D43.3D49.7
nerve (ganglion) abducensC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) accessory (spinal)C72.59C79.49D33.3D43.3D49.7
nerve (ganglion) acousticC72.4C79.49D33.3D43.3D49.7
nerve (ganglion) auditoryC72.4C79.49D33.3D43.3D49.7
nerve (ganglion) cranialC72.50C79.49D33.3D43.3D49.7
nerve (ganglion) cranial specified NECC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) facialC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) glossopharyngealC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) hypoglossalC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) oculomotorC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) olfactoryC47.2C79.49D33.3D43.3D49.7
nerve (ganglion) opticC72.3C79.49D33.3D43.3D49.7
nerve (ganglion) spinal NEC accessoryC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) trigeminalC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) trochlearC72.59C79.49D33.3D43.3D49.7
nerve (ganglion) vagusC72.59C79.49D33.3D43.3D49.7
olfactory nerve or bulbC72.2C79.49D33.3D43.3D49.7
optic nerve, chiasm, or tractC72.3C79.49D33.3D43.3D49.7

Patient EducationClinical

Benign Tumors

Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D33.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
225.1 Benign neo cranial nerve
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D33.3Overview

Is D33.3 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report benign neoplasm of cranial nerves on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of D33.3?

Under the General Equivalence Mappings, benign neoplasm of cranial nerves converts to ICD-9-CM 225.1 (benign neo cranial nerve). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.