ICD-10-CM Code D18.0


Version 2021 Non-Billable Code

Not Valid for Submission

D18.0 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of hemangioma. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions.

Short Description:Hemangioma
Long Description:Hemangioma

Consider the following ICD-10 codes with a higher level of specificity:

  • D18.00 - Hemangioma unspecified site
  • D18.01 - Hemangioma of skin and subcutaneous tissue
  • D18.02 - Hemangioma of intracranial structures
  • D18.03 - Hemangioma of intra-abdominal structures
  • D18.09 - Hemangioma of other sites

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code D18.0:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Angioma NOS
  • Cavernous nevus

Clinical Information

  • ENCHONDROMATOSIS-. benign growths of cartilage in the metaphyses of several bones.
  • HEMANGIOMA-. a vascular anomaly due to proliferation of blood vessels that forms a tumor like mass. the common types involve capillaries and veins. it can occur anywhere in the body but is most frequently noticed in the skin and subcutaneous tissue. from stedman 27th ed 2000
  • HEMANGIOMA CAVERNOUS-. a vascular anomaly that is a collection of tortuous blood vessels and connective tissue. this tumor like mass with the large vascular space is filled with blood and usually appears as a strawberry like lesion in the subcutaneous areas of the face extremities or other regions of the body including the central nervous system.
  • STURGE WEBER SYNDROME-. a non inherited congenital condition with vascular and neurological abnormalities. it is characterized by facial vascular nevi port wine stain and capillary angiomatosis of intracranial membranes meninges; choroid. neurological features include epilepsy; cognitive deficits; glaucoma; and visual defects.
  • GRANULOMA PYOGENIC-. a disorder of the skin the oral mucosa and the gingiva that usually presents as a solitary polypoid capillary hemangioma often resulting from trauma. it is manifested as an inflammatory response with similar characteristics to those of a granuloma.
  • HISTIOCYTOMA BENIGN FIBROUS-. a benign tumor composed wholly or in part of cells with the morphologic characteristics of histiocytes and with various fibroblastic components. fibrous histiocytomas can occur anywhere in the body. when they occur in the skin they are called dermatofibromas or sclerosing hemangiomas. from devita jr et al. cancer: principles & practice of oncology 5th ed p1747
  • HEMANGIOMA CAPILLARY-. a dull red firm dome shaped hemangioma sharply demarcated from surrounding skin usually located on the head and neck which grows rapidly and generally undergoes regression and involution without scarring. it is caused by proliferation of immature capillary vessels in active stroma and is usually present at birth or occurs within the first two or three months of life. dorland 27th ed
  • BRANCHIO OTO RENAL SYNDROME-. an autosomal dominant disorder manifested by various combinations of preauricular pits branchial fistulae or cysts lacrimal duct stenosis hearing loss structural defects of the outer middle or inner ear and renal dysplasia. associated defects include asthenic habitus long narrow facies constricted palate deep overbite and myopia. hearing loss may be due to mondini type cochlear defect and stapes fixation. jablonski's dictionary of syndromes & eponymic diseases 2d ed
  • HEMANGIOMA CAVERNOUS CENTRAL NERVOUS SYSTEM-. a vascular anomaly composed of a collection of large thin walled tortuous veins that can occur in any part of the central nervous system but lack intervening nervous tissue. familial occurrence is common and has been associated with a number of genes mapped to 7q 7p and 3q. clinical features include seizures; headache; stroke; and progressive neurological deficit.
  • PULMONARY SCLEROSING HEMANGIOMA-. a benign neoplasm of pneumocytes cells of the pulmonary alveoli. originally considered to be vascular in origin it is now classified as an epithelial tumor with several elements including solid cellular areas papillary structure sclerotic regions and dilated blood filled spaces resembling hemangioma.
  • KASABACH MERRITT SYNDROME-. rapidly growing vascular lesion along the midline axis of the neck upper trunk and extremities that is characterized by consumption coagulopathy; thrombocytopenia; and hemolytic anemia. it is often associated with infantile kaposiform hemangioendothelioma and other vascular tumors such as tufted angioma.

Code Classification

  • Neoplasms (C00–D48)
    • Benign neoplasms, except benign neuroendocrine tumors (D10-D36)
      • Hemangioma and lymphangioma, any site (D18)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients

Benign Tumors

Also called: Benign neoplasms, Noncancerous tumors

Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.

Tumors are made up of extra cells. Normally, cells grow and divide to form new cells as your body needs them. When cells grow old, they die, and new cells take their place. Sometimes, this process goes wrong. New cells form when your body does not need them, and old cells do not die when they should. These extra cells can divide without stopping and may form tumor.

Treatment often involves surgery. Benign tumors usually don't grow back.

NIH: National Cancer Institute

  • Biopsy - polyps (Medical Encyclopedia)
  • Cherry angioma (Medical Encyclopedia)

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Also called: Cafe au lait spot, Hemangioma, Mongolian spot, Nevus, Strawberry mark

Birthmarks are abnormalities of the skin that are present when a baby is born. There are two types of birthmarks. Vascular birthmarks are made up of blood vessels that haven't formed correctly. They are usually red. Two types of vascular birthmarks are hemangiomas and port-wine stains. Pigmented birthmarks are made of a cluster of pigment cells which cause color in skin. They can be many different colors, from tan to brown, gray to black, or even blue. Moles can be birthmarks.

No one knows what causes many types of birthmarks, but some run in families. Your baby's doctor will look at the birthmark to see if it needs any treatment or if it should be watched. Pigmented birthmarks aren't usually treated, except for moles. Treatment for vascular birthmarks includes laser surgery.

Most birthmarks are not serious, and some go away on their own. Some stay the same or get worse as you get older. Usually birthmarks are only a concern for your appearance. But certain types can increase your risk of skin cancer. If your birthmark bleeds, hurts, itches, or becomes infected, call your health care provider.

  • Birthmarks - pigmented (Medical Encyclopedia)
  • Birthmarks - red (Medical Encyclopedia)
  • Cherry angioma (Medical Encyclopedia)
  • Hemangioma (Medical Encyclopedia)
  • Mongolian blue spots (Medical Encyclopedia)
  • Port-wine stain (Medical Encyclopedia)
  • Stork bite (Medical Encyclopedia)

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Vascular Diseases

What are vascular diseases?

Your vascular system is your body's network of blood vessels. It includes your

  • Arteries, which carry oxygen-rich blood from your heart to your tissues and organs
  • Veins, which carry the blood and waste products back to your heart
  • Capillaries, which are tiny blood vessels that connect your small arteries to your small veins. The walls of the capillaries are thin and leaky, to allow for an exchange of materials between your tissues and blood.

Vascular diseases are conditions which affect your vascular system. They are common and can be serious. Some types include

  • Aneurysm - a bulge or "ballooning" in the wall of an artery
  • Atherosclerosis - a disease in which plaque builds up inside your arteries. Plaque is made up of fat, cholesterol, calcium, and other substances found in the blood.
  • Blood clots, including deep vein thrombosis and pulmonary embolism
  • Coronary artery disease and carotid artery disease, diseases that involve the narrowing or blockage of an artery. The cause is usually a buildup of plaque.
  • Raynaud's disease - a disorder that causes the blood vessels to narrow when you are cold or feeling stressed
  • Stroke - a serious condition that happens when blood flow to your brain stops.
  • Varicose veins - swollen, twisted veins that you can see just under the skin
  • Vasculitis - inflammation of the blood vessels

What causes vascular diseases?

The causes of vascular diseases depend on the specific disease. These causes include

  • Genetics
  • Heart diseases such as high cholesterol and high blood pressure
  • Infection
  • Injury
  • Medicines, including hormones

Sometimes the cause is unknown.

Who is at risk for vascular diseases?

The risk factors for vascular diseases can vary, depending on the specific disease. But some of the more common risk factors include

  • Age - your risk of some diseases goes up as you get older
  • Conditions that can affect the heart and blood vessels, such as diabetes or high cholesterol
  • Family history of vascular or heart diseases
  • Infection or injury that damages your veins
  • Lack of exercise
  • Obesity
  • Pregnancy
  • Sitting or standing still for long periods of time
  • Smoking

What are the symptoms of vascular diseases?

The symptoms for each disease are different.

How are vascular diseases diagnosed?

To make a diagnosis, your health care provider will do a physical exam and ask about your symptoms and medical history. You may have imaging tests and/or blood tests.

How are vascular diseases treated?

Which treatment you get depends on which vascular disease you have and how severe it is. Types of treatments for vascular diseases include

  • Lifestyle changes, such as eating a heart-healthy diet and getting more exercise
  • Medicines, such as blood pressure medicines, blood thinners, cholesterol medicines, and clot-dissolving drugs. In some cases, providers use a catheter to send medicine directly to a blood vessel.
  • Non-surgical procedures, such as angioplasty, stenting, and vein ablation
  • Surgery

Can vascular diseases be prevented?

There are steps you can take to help prevent vascular diseases:

  • Make healthy lifestyle changes, such as eating a heart-healthy diet and getting more exercise
  • Don't smoke. If you are already a smoker, talk to your health care provider for help in finding the best way for you to quit.
  • Keep your blood pressure and cholesterol in check
  • If you have diabetes, control your blood sugar
  • Try not to sit or stand for up long periods of time. If you do need to sit all day, get up and move around every hour or so. If you traveling on a long trip, you can also wear compression stockings and regularly stretch your legs.
  • Aortic arch syndrome (Medical Encyclopedia)
  • Arterial embolism (Medical Encyclopedia)
  • Arteriogram (Medical Encyclopedia)
  • Cerebral angiography (Medical Encyclopedia)
  • Duplex ultrasound (Medical Encyclopedia)
  • Venous insufficiency (Medical Encyclopedia)
  • Venous ulcers -- self-care (Medical Encyclopedia)

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