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  5. Hemangioma and lymphangioma, any site (D18)

Hemangioma and lymphangioma, any site (D18)

The ICD-10 codes beginning with D18 are specifically used to classify benign tumors known as hemangiomas and lymphangiomas, which can develop in various parts of the body. These codes help accurately identify the type and location of these vascular growths for medical documentation and treatment planning.

Hemangiomas, also called blood vessel tumors, are represented by codes such as D18.0 for general hemangioma and are further specified by site. For example, D18.01 corresponds to hemangiomas of the skin and subcutaneous tissue, including conditions like infantile hemangioma and strawberry nevus. Hemangiomas of intracranial structures (brain), intra-abdominal organs (like liver and spleen), and other less common sites have distinct codes (D18.02, D18.03, and D18.09). These synonyms and varying presentations help medical coders select the right ICD-10 code for hemangioma cases. Likewise, D18.1 identifies lymphangiomas, benign growths of lymphatic vessels, which can affect areas such as the skin, liver, or larynx and are sometimes called cystic hygromas or lymphangiomatosis. Using these detailed codes ensures precise recognition of these vascular conditions in health records and claims.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • benign neoplasm of glomus jugulare D35.6
  • blue or pigmented nevus D22
  • nevus NOS D22
  • vascular nevus Q82.5

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Angiolymphoid Hyperplasia with Eosinophilia

Solitary or multiple benign cutaneous nodules comprised of immature and mature vascular structures intermingled with endothelial cells and a varied infiltrate of eosinophils, histiocytes, lymphocytes, and mast cells.

Blood Vessels

Any of the tubular vessels conveying the blood (arteries, arterioles, capillaries, venules, and veins).

Branchio-Oto-Renal Syndrome

An autosomal dominant disorder manifested by various combinations of preauricular pits, branchial fistulae or cysts, lacrimal duct stenosis, hearing loss, structural defects of the outer, middle, or inner ear, and renal dysplasia. Associated defects include asthenic habitus, long narrow facies, constricted palate, deep overbite, and myopia. Hearing loss may be due to Mondini type cochlear defect and stapes fixation. (Jablonski's Dictionary of Syndromes & Eponymic Diseases, 2d ed)

Castleman Disease

Large benign, hyperplastic lymph nodes. The more common hyaline vascular subtype is characterized by small hyaline vascular follicles and interfollicular capillary proliferations. Plasma cells are often present and represent another subtype with the plasma cells containing IgM and IMMUNOGLOBULIN A.

Enchondromatosis

Benign growths of cartilage in the metaphyses of several bones.

Granuloma, Pyogenic

A disorder of the skin, the oral mucosa, and the gingiva, that usually presents as a solitary polypoid capillary hemangioma often resulting from trauma. It is manifested as an inflammatory response with similar characteristics to those of a granuloma.

Hemangioma

A vascular anomaly due to proliferation of BLOOD VESSELS that forms a tumor-like mass. The common types involve CAPILLARIES and VEINS. It can occur anywhere in the body but is most frequently noticed in the SKIN and SUBCUTANEOUS TISSUE. (from Stedman, 27th ed, 2000)

Hemangioma, Capillary

A dull red, firm, dome-shaped hemangioma, sharply demarcated from surrounding skin, usually located on the head and neck, which grows rapidly and generally undergoes regression and involution without scarring. It is caused by proliferation of immature capillary vessels in active stroma, and is usually present at birth or occurs within the first two or three months of life. (Dorland, 27th ed)

Hemangioma, Cavernous

A vascular anomaly that is a collection of tortuous BLOOD VESSELS and connective tissue. This tumor-like mass with the large vascular space is filled with blood and usually appears as a strawberry-like lesion in the subcutaneous areas of the face, extremities, or other regions of the body including the central nervous system.

Hemangioma, Cavernous, Central Nervous System

A vascular anomaly composed of a collection of large, thin walled tortuous VEINS that can occur in any part of the central nervous system but lack intervening nervous tissue. Familial occurrence is common and has been associated with a number of genes mapped to 7q, 7p and 3q. Clinical features include SEIZURES; HEADACHE; STROKE; and progressive neurological deficit.

Histiocytes

Macrophages found in the TISSUES, as opposed to those found in the blood (MONOCYTES) or serous cavities (SEROUS MEMBRANE).

Histiocytoma, Benign Fibrous

A benign tumor composed, wholly or in part, of cells with the morphologic characteristics of HISTIOCYTES and with various fibroblastic components. Fibrous histiocytomas can occur anywhere in the body. When they occur in the skin, they are called dermatofibromas or sclerosing hemangiomas. (From DeVita Jr et al., Cancer: Principles & Practice of Oncology, 5th ed, p1747)

Kasabach-Merritt Syndrome

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

Lymphangioma

A benign tumor resulting from a congenital malformation of the lymphatic system. Lymphangioendothelioma is a type of lymphangioma in which endothelial cells are the dominant component.

Lymphangioma, Cystic

A cystic growth originating from lymphatic tissue. It is usually found in the neck, axilla, or groin.

Pulmonary Sclerosing Hemangioma

A benign neoplasm of pneumocytes, cells of the PULMONARY ALVEOLI. Originally considered to be vascular in origin, it is now classified as an epithelial tumor with several elements, including solid cellular areas, papillary structure, sclerotic regions, and dilated blood-filled spaces resembling HEMANGIOMA.

Sturge-Weber Syndrome

A non-inherited congenital condition with vascular and neurological abnormalities. It is characterized by facial vascular nevi (PORT-WINE STAIN), and capillary angiomatosis of intracranial membranes (MENINGES; CHOROID). Neurological features include EPILEPSY; cognitive deficits; GLAUCOMA; and visual defects.