ICD-10-CM Excludes2 Notes · Chapter 17 · FY 2027 Q00-QA1

Excludes2 Notes in Chapter 17: Congenital malformations, deformations and chromosomal abnormalities ICD-10-CM

An Excludes2 note means "NOT INCLUDED HERE": the excluded condition is not part of this code, but a patient may have both, so both codes may be reported. In Chapter 17 (Q00-QA1), notes printed in the chapter name other codes 53 times, and Excludes2 Notes anywhere in the Tabular List name the chapter’s codes 74 times, covering 49 distinct codes, categories and ranges. Switch views to read the list either way.

✓ From the official FY 2027 ICD-10-CM Tabular ListDefinitions follow the Official Guidelines, Section I.A
53
References in Its Notes
74
References to Its Codes
49
Chapter Codes Named
Q00-QA1
Chapter 17
Chapter 17

Excludes2 Notes by the code that carries the note

23 of 23 shown
  • Chapter note Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
    • inborn errors of metabolism (E70-E88)
  • Q07 Other congenital malformations of nervous system applies to 6 codes
    • congenital central alveolar hypoventilation syndrome (G47.35)
    • familial dysautonomia [Riley-Day] (G90.1)
    • neurofibromatosis (nonmalignant) (Q85.0-)
  • Block note Block Q10-Q18 Congenital malformations of eye, ear, face and neck applies to 62 codes
    • cleft lip and cleft palate (Q35-Q37)
    • congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
    • congenital malformation of larynx (Q31.-)
    • congenital malformation of lip NEC (Q38.0)
    • congenital malformation of nose (Q30.-)
    • congenital malformation of parathyroid gland (Q89.2)
    • congenital malformation of thyroid gland (Q89.2)
  • Q14 Congenital malformations of posterior segment of eye applies to 6 codes
  • Q21.1 Atrial septal defect applies to 8 codes
    • ostium primum atrial septal defect (type I) (Q21.20)
  • Q27 Other congenital malformations of peripheral vascular system applies to 12 codes
    • anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
    • anomalies of coronary vessels (Q24.5)
    • anomalies of pulmonary artery (Q25.5-Q25.7)
    • congenital retinal aneurysm (Q14.1)
    • hemangioma and lymphangioma (D18.-)
  • Q27.3 Arteriovenous malformation (peripheral) applies to 6 codes
    • arteriovenous malformation of cerebral vessels (Q28.2)
    • arteriovenous malformation of precerebral vessels (Q28.0)
  • Q28 Other congenital malformations of circulatory system applies to 6 codes
    • congenital peripheral aneurysm (Q27.8)
    • congenital pulmonary aneurysm (Q25.79)
    • congenital retinal aneurysm (Q14.1)
  • Q28.8 Other specified congenital malformations of circulatory system
    • disorders of pyrophosphate metabolism (E83.82-)
  • Q34 Other congenital malformations of respiratory system applies to 4 codes
    • congenital central alveolar hypoventilation syndrome (G47.35)
  • Block note Block Q35-Q37 Cleft lip and cleft palate applies to 16 codes
  • Q45 Other congenital malformations of digestive system applies to 6 codes
    • congenital diaphragmatic hernia (Q79.0)
    • congenital hiatus hernia (Q40.1)
  • Q68 Other congenital musculoskeletal deformities applies to 8 codes
    • congenital myotonic chondrodystrophy (G71.13)
  • Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine applies to 10 codes
    • congenital myotonic chondrodystrophy (G71.13)
  • Q78 Other osteochondrodysplasias applies to 9 codes
    • congenital myotonic chondrodystrophy (G71.13)
  • Q79 Congenital malformations of musculoskeletal system, not elsewhere classified applies to 14 codes
    • congenital (sternomastoid) torticollis (Q68.0)
  • Q82.5 Congenital non-neoplastic nevus
  • Q82.6 Congenital sacral dimple
    • pilonidal cyst with abscess (L05.01)
    • pilonidal cyst without abscess (L05.91)
  • Q82.8 Other specified congenital malformations of skin
    • disorders of pyrophosphate metabolism (E83.82-)
  • Q83 Congenital malformations of breast applies to 6 codes
  • Q86 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified applies to 4 codes
    • iodine-deficiency-related hypothyroidism (E00-E02)
    • nonteratogenic effects of substances transmitted via placenta or breast milk (P04.-)
  • Block note Block Q90-Q99 Chromosomal abnormalities, not elsewhere classified applies to 74 codes
    • mitochondrial metabolic disorders (E88.4-)
  • QA1 Genetic disorders associated with neoplasms, not elsewhere classified applies to 5 codes
    • multiple endocrine neoplasia [MEN] syndromes (E31.2-)

The first view lists notes printed in this chapter (a note on a category or block applies to every code beneath it). The second lists codes of this chapter named by Excludes2 Notes anywhere in the Tabular List, including notes in other chapters.

Questions About Excludes2 Notes

What does an Excludes2 note mean?

An Excludes2 note means “Not included here”: the excluded condition is not part of the condition represented by the code, but a patient may have both conditions at the same time (Section I.A.12.b). The FY 2027 Tabular List has 2,529 of them; 2,493 name other codes, with 2,799 references to 1,779 distinct codes, categories and ranges.

Can both codes be reported when there is an Excludes2 note?

Yes. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate: that is, when the patient has both conditions and both are documented.

Related References

ICD-10-CM Official GuidelinesICD-10-CM Code LookupICD-10-CM Codes ListCode Lists by Tag

Source: FY 2027 ICD-10-CM Tabular List (CMS and NCHS) and the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027, Section I.A. ICD List is not affiliated with CMS or NCHS.