2026 ICD-10-CM Diagnosis Code Z83.42Family history of familial hypercholesterolemia

ICD-10-CM Codes›Z00–Z99›Z77-Z99›Z83

ICD-10-CM Z83.42
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Z83.42 is a billable ICD-10-CM diagnosis code for family history of familial hypercholesterolemia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is not accepted as a principal diagnosis by the Medicare Code Editor and exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Family history of disease.

Code Identity

ICD-10-CM Code
Z83.42
Billable Status
Yes — Valid for Submission
Code Describes
Family history of familial hypercholesterolemia
Short Description
Family history of familial hypercholesterolemia
Same as the full description in the CMS dataset.
Parent Code
Z83.4
Family history of other endocrine, nutritional and metabolic diseases

Code Classification

ChapterZ00–Z99Factors influencing health status and contact with health services
SectionZ77-Z99Persons with potential health hazards related to family and personal history and certain conditions influencing health status
CategoryZ83Family history of other specific disorders
This CodeZ83.42Family history of familial hypercholesterolemia

Code EditsBilling

Medicare Code Editor checks that affect claim validity for Z83.42.

Unacceptable principal diagnosis
There are selected codes that describe a circumstance which influences an individual's health status but not a current illness or injury, or codes that are not specific manifestations but may be due to an underlying cause. These codes are considered unacceptable as a principal diagnosis.

Present on Admission (POA)Billing

Z83.42 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Family history of double heterozygous familial hypercholesterolemia
  • Family history of familial hypercholesterolemia
  • Family history of Fredrickson type IIa hyperlipoproteinemia
  • Family history of hyperlipidemia
  • FH: Hypercholesterolemia
  • FH: Raised blood lipids

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • History
      • family (of)
        • disease or disorder (of)
          • familial hypercholesterolemia
    • History
      • family (of)
        • familial hypercholesterolemia

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR FAC028
Family history of disease
Default principal diagnosis: inpatient No · outpatient Yes

Patient EducationClinical

Cholesterol

Cholesterol is a waxy, fat-like substance that's found in all the cells in your body. Your body needs some cholesterol to make hormones, vitamin D, and substances that help you digest foods. Your body makes all the cholesterol it needs. Cholesterol is also found in foods from animal sources, such as egg yolks, meat, and cheese.

The full article covers:

  • What is cholesterol?
  • What are HDL, LDL, and VLDL?
  • What causes high cholesterol?
  • What can raise my risk of high cholesterol?
  • What other health problems can high cholesterol cause?
  • How is high cholesterol diagnosed?
  • How can I lower my cholesterol?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Z83.42 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
V18.19 Fm hx endo/metab dis NEC
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement Z83.42 replaces the following previously assigned code(s):

  • Z83.49 - Family history of endo, nutritional and metabolic diseases
FY 2018AddedAdded to the ICD-10-CM code setEffective October 1, 2017.
FY 2019–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Z83.42Overview

Is Z83.42 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report family history of familial hypercholesterolemia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Can Z83.42 be a principal diagnosis?

No. The Medicare Code Editor rejects this code as a principal diagnosis because family history of familial hypercholesterolemia describes a circumstance that influences health status rather than a current illness. Report it as a secondary diagnosis.

Is Z83.42 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for family history of familial hypercholesterolemia on inpatient claims.

What is the ICD-9 equivalent of Z83.42?

Under the General Equivalence Mappings, family history of familial hypercholesterolemia converts to ICD-9-CM V18.19 (fm hx endo/metab dis NEC). The mapping is approximate, so confirm the match fits the documentation.