2026 ICD-10-CM Diagnosis Code Q99.812Usher syndrome, type 2

ICD-10-CM Codes›Q00-Q99›Q90-Q99›Q99

ICD-10-CM Q99.812
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q99.812 is a billable ICD-10-CM diagnosis code for usher syndrome, type 2. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting.

Code Identity

ICD-10-CM Code
Q99.812
Billable Status
Yes — Valid for Submission
Code Describes
Usher syndrome, type 2
Short Description
Usher syndrome, type 2
Same as the full description in the CMS dataset.
Parent Code
Q99.81
Usher syndrome

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ90-Q99Chromosomal abnormalities, not elsewhere classified
CategoryQ99Other chromosome abnormalities, not elsewhere classified
This CodeQ99.812Usher syndrome, type 2

Present on Admission (POA)Billing

Q99.812 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • usher
        • type 2

Clinical InformationClinical

  • Usher Syndrome Type 2

    a syndrome characterized by congenital, bilateral sensorineural hearing loss that is mild to moderate in the low frequencies and severe to profound in the higher frequencies, no abnormalities in the vestibular system, and retinitis pigmentosa.

  • Usher Syndrome Type 2C|USH2C

    an autosomal recessive sub-type of usher syndrome caused by homozygous or compound heterozygous mutation(s) in the adgrv1 gene, encoding adhesion g protein-coupled receptor v1. it may also result from biallelic digenic mutation(s) in adgrv1 and pdzd7, which encodes pdz domain-containing protein 7.

Code History & ChangesHistory

New Code Q99.812 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.

Replacement Q99.812 replaces the following previously assigned code(s):

  • Q99.8 - Other specified chromosome abnormalities
FY 2026AddedAdded to the ICD-10-CM code setEffective October 1, 2025.
FY 2026CurrentRevised in the current code setEffective October 1, 2025 through September 30, 2026.

Questions About Q99.812Overview

Is Q99.812 (Usher syndrome) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report usher syndrome, type 2 on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q99.812 group to?

When usher syndrome, type 2 is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q99.812 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for usher syndrome, type 2 on inpatient claims.